Document Detail


Treatment of the craniofacial complications of Beckwith-Wiedemann syndrome.
MedLine Citation:
PMID:  7604127     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Variable degrees of macroglossia have been noted in patients with Beckwith-Wiedemann syndrome. Past studies have shown that a major effect of the macroglossia is protrusion of dentoalveolar structures, resulting in an anterior open bite and a prognathic mandibular appearance secondary to an abnormally obtuse gonial angle and increased effective mandibular length. In our series of 11 Beckwith-Wiedemann syndrome patients we have observed that early correction of the macroglossia by means of partial glossectomy has resulted in decreased anterior open bite and mandibular prognathism as compared with patients managed conservatively.
Authors:
R M Menard; J Delaire; S A Schendel
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Plastic and reconstructive surgery     Volume:  96     ISSN:  0032-1052     ISO Abbreviation:  Plast. Reconstr. Surg.     Publication Date:  1995 Jul 
Date Detail:
Created Date:  1995-08-09     Completed Date:  1995-08-09     Revised Date:  2011-02-16    
Medline Journal Info:
Nlm Unique ID:  1306050     Medline TA:  Plast Reconstr Surg     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  27-33     Citation Subset:  AIM; IM    
Affiliation:
Division of Plastic and Reconstructive Surgery, Stanford University School of Medicine, Calif, USA.
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MeSH Terms
Descriptor/Qualifier:
Beckwith-Wiedemann Syndrome / pathology,  physiopathology,  surgery*
Cephalometry
Child
Child, Preschool
Glossectomy / methods
Humans
Infant
Macroglossia / surgery*
Maxillofacial Development

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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