| Transient exacerbation of hemiplegia following minor head trauma in Sturge-Weber syndrome. | |
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MedLine Citation:
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PMID: 17718827 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Sturge-Weber syndrome (SWS) is a sporadic disorder characterized by naevus (port wine stain), a pial angioma, and glaucoma. The angioma comprises abnormal tortuous vessels on the leptomeninges with underlying brain gliosis, calcification, and atrophy. The cerebral angioma is commonly unilateral but may be bilateral. Hemiplegia usually follows recurrent hemiconvulsions and may be related to venous stasis. The hemiplegia can be static, progressive, or fluctuating. Transient worsening of the hemiplegia can be seen with seizures and episodes resembling hemiplegic migraine. We report five patients (four females, one male) with SWS who have had transient worsening of hemiplegia following minor head injuries, occurring between the ages of 10 months and 12 years (median age 4y 6mo). An additional pilot survey suggests that this may affect up to 20% of patients. |
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Authors:
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Z Zolkipli; S Aylett; P M Rankin; B G R Neville |
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Publication Detail:
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Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't |
Journal Detail:
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Title: Developmental medicine and child neurology Volume: 49 ISSN: 0012-1622 ISO Abbreviation: Dev Med Child Neurol Publication Date: 2007 Sep |
Date Detail:
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Created Date: 2007-08-27 Completed Date: 2007-10-02 Revised Date: 2009-11-11 |
Medline Journal Info:
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Nlm Unique ID: 0006761 Medline TA: Dev Med Child Neurol Country: England |
Other Details:
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Languages: eng Pagination: 697-9 Citation Subset: IM |
Affiliation:
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Department of Paediatric Neurology, Great Ormond Street Hospital/Cognitive Neurosciences Unit, UCL Institute of Child Health, London, UK. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Acute Disease Adolescent Adult Child Child, Preschool Craniocerebral Trauma / complications*, physiopathology Female Hemiplegia / etiology*, physiopathology Humans Male Psychomotor Performance Sturge-Weber Syndrome / complications*, physiopathology |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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