| Total knee arthroplasty in a patient with pseudopseudohypoparathyroidism. | |
| | |
MedLine Citation:
|
PMID: 21815586 Owner: NLM Status: In-Data-Review |
Abstract/OtherAbstract:
|
Pseudopseudohypoparathyroidism (PPH) is a rare genetic disorder characterized by multiple musculoskeletal anomalies and normal serum calcium, phosphate, and parathyroid hormone levels. Although the musculoskeletal manifestations of PPH are well known, little has been reported on the management of orthopedic problems. We report a case of total knee arthroplasty (TKA) performed in a patient with PPH. To our knowledge, this case is not only unique to the arthroplasty literature but is the first report of its kind. This report illustrates the unique pathoanatomy of PPH, the medical and surgical management required, and a previously unreported musculoskeletal abnormality associated with PPH: synovial osteochondromatosis of the knee.Common musculoskeletal anomalies associated with PPH include shortening/bowing of long bones; shortening of metacarpals, metatarsals, and/or phalanges; exostoses; calcification/ossification of subcutaneous and/or periarticular soft tissues; a thickened calvarium; microcephaly; bony coalitions of the hand; vertebral column abnormalities; cubitus valgus; radius/ulna curvus; coxa vara; coxa valga; and genu valgum. This case is the first to report an association of synovial osteochondromatosis with PPH. Because synovial osteochondromatosis and PPH share a common disorder of soft tissue calcification/ossification, as well as abnormal bone formation, this clinical finding does not seem merely coincidental. |
| | |
Authors:
|
Michael R Fraser; V Franklin Sechriest |
Related Documents
:
|
8435126 - Upper airway obstruction--an unusual complication following a minor scalding injury. 840566 - Hexachlorophene storage in a burn patient associated with encephalopathy. 20683196 - Paraneoplastic pemphigus in a burn intensive care unit: case report and review of the l... 9215196 - Brachial plexus palsy: an old problem revisited again. ii. cases in point. 1771466 - Symptomatic spinal epidural lipomatosis induced by a long-term steroid treatment. revie... 16009406 - Metastatic testicular seminoma to the prostate. |
Publication Detail:
|
Type: Journal Article Date: 2011-08-08 |
Journal Detail:
|
Title: Orthopedics Volume: 34 ISSN: 1938-2367 ISO Abbreviation: Orthopedics Publication Date: 2011 |
Date Detail:
|
Created Date: 2011-08-05 Completed Date: - Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 7806107 Medline TA: Orthopedics Country: United States |
Other Details:
|
Languages: eng Pagination: e413-7 Citation Subset: IM |
Copyright Information:
|
Copyright 2011, SLACK Incorporated. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
|
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Three cases of slipped capital femoral epiphysis in one family.
Next Document: Pigmented Villonodular Synovitis After TKA Associated With Tibial Component Loosening.