| Tetralogy of Fallot with absent pulmonary valve syndrome. | |
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MedLine Citation:
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PMID: 15283354 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Tetralogy of Fallot with absent pulmonary valve syndrome is a rare variant of tetralogy of Fallot marked by severe pulmonary insufficiency in utero and significant, sometimes massive, dilation of the pulmonary arteries. This syndrome can be associated with airway abnormalities that can cause respiratory compromise. Patients who present with respiratory symptoms early in life continue to present a major clinical challenge associated with relatively high mortality rates, typically in the 20% to 30% range. A variety of surgical techniques have been developed to address absent pulmonary valve syndrome that may improve long-term outcomes. |
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Authors:
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Paul M Kirshbom; Brian E Kogon |
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Publication Detail:
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Type: Journal Article; Review |
Journal Detail:
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Title: Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annual Volume: 7 ISSN: 1092-9126 ISO Abbreviation: Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu Publication Date: 2004 |
Date Detail:
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Created Date: 2004-07-30 Completed Date: 2004-09-28 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 9815944 Medline TA: Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu Country: United States |
Other Details:
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Languages: eng Pagination: 65-71 Citation Subset: IM |
Affiliation:
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Division of Cardiothoracic Surgery, Emory University School of Medicine, Atlanta, GA, USA. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Child, Preschool Humans Infant Infant, Newborn Pulmonary Valve / abnormalities* Pulmonary Valve Insufficiency / complications, congenital, physiopathology, therapy* Tetralogy of Fallot / complications, physiopathology*, therapy* Treatment Outcome |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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