| A teenager with Marfan syndrome and left ventricular noncompaction. | |
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MedLine Citation:
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PMID: 19795159 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We report a teenager with Marfan syndrome who presented to Cincinnati Children's Hospital Medical Center as part of a preoperative evaluation for an orthopedic procedure after asymptomatic arrhythmia was recognized. Continuous cardiac monitoring showed frequent premature ventricular contractions and nonsustained runs of ventricular tachycardia. Cardiac magnetic resonance imaging showed left ventricular noncompaction (LVNC), prompting insertion of an implantable cardiac defibrillator. Although Marfan syndrome is associated with cardiac lesions, it has not previously been described with LVNC. Likewise LVNC has been seen in association with other cardiac lesions; however, this report represents the first reference of LVNC in the context of Marfan syndrome. |
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Authors:
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David Kwiatkowski; Sean Hagenbuch; Richard Meyer |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2009-10-01 |
Journal Detail:
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Title: Pediatric cardiology Volume: 31 ISSN: 1432-1971 ISO Abbreviation: Pediatr Cardiol Publication Date: 2010 Jan |
Date Detail:
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Created Date: 2010-01-21 Completed Date: 2010-04-13 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 8003849 Medline TA: Pediatr Cardiol Country: United States |
Other Details:
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Languages: eng Pagination: 132-5 Citation Subset: IM |
Affiliation:
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Department of Pediatrics, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Arrhythmias, Cardiac / etiology*, pathology, therapy Cardiomyopathies / congenital*, pathology, therapy Defibrillators, Implantable Electrocardiography Female Heart Ventricles / abnormalities* Humans Magnetic Resonance Imaging Marfan Syndrome / complications* Ventricular Dysfunction, Left / etiology*, pathology, therapy |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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