Document Detail


Targeted expression of a dominant negative FGF receptor blocks branching morphogenesis and epithelial differentiation of the mouse lung.
MedLine Citation:
PMID:  8045260     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Mouse lung development begins when two lung buds sprout from the epithelium of the embryonic gut. Patterning of the airways is then accomplished by the outgrowth and repetitive branching of the two lung buds, a process called branching morphogenesis. One of the four fibroblast growth factor (FGF) receptor genes, FGFR2, is expressed in the epithelium of a number of embryonic organs including the lung buds. To block the function of FGFR2 during branching morphogenesis of the lung without affecting its function in other embryonic tissues, the human surfactant protein C promoter was used to target expression of a dominant negative FGFR2 exclusively to lung bud epithelium in transgenic mice. Newborn mice expressing the transgene were completely normal except that instead of normally developed lungs they had two undifferentiated epithelial tubes that extended from the bifurcation of the trachea down to the diaphragm, a defect that resulted in perinatal death. Thus, the dominant negative FGF receptor completely blocked airway branching and epithelial differentiation, without prohibiting outgrowth, establishing a specific role for FGFs in branching morphogenesis of the mammalian lung.
Authors:
K Peters; S Werner; X Liao; S Wert; J Whitsett; L Williams
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  The EMBO journal     Volume:  13     ISSN:  0261-4189     ISO Abbreviation:  EMBO J.     Publication Date:  1994 Jul 
Date Detail:
Created Date:  1994-09-01     Completed Date:  1994-09-01     Revised Date:  2012-06-05    
Medline Journal Info:
Nlm Unique ID:  8208664     Medline TA:  EMBO J     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  3296-301     Citation Subset:  IM    
Affiliation:
Program of Excellence in Molecular Biology, University of California at San Francisco 94143-0130.
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MeSH Terms
Descriptor/Qualifier:
Animals
Bronchi / anatomy & histology,  embryology
Cell Differentiation
Epithelium / embryology
Gene Expression Regulation
Humans
Lung / anatomy & histology,  embryology*
Mice
Mice, Transgenic
Microtomy / methods
Morphogenesis
Receptor Protein-Tyrosine Kinases / genetics*
Receptor, Fibroblast Growth Factor, Type 2
Receptors, Fibroblast Growth Factor / genetics*
Trachea / anatomy & histology,  embryology*
Chemical
Reg. No./Substance:
0/Receptors, Fibroblast Growth Factor; EC 2.7.10.1/FGFR2 protein, human; EC 2.7.10.1/Fgfr2 protein, mouse; EC 2.7.10.1/Receptor Protein-Tyrosine Kinases; EC 2.7.10.1/Receptor, Fibroblast Growth Factor, Type 2
Comments/Corrections

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