Document Detail


Takayasu's arteritis associated with Wiskott-Aldrich syndrome.
MedLine Citation:
PMID:  1356386     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A unique case of a Chinese boy with Wiskott-Aldrich syndrome (WAS) associated with Takayasu's arteritis is reported. He had eczema, epistaxis and recurrent infections since early infancy and was found to have thrombocytopenia, negative delayed-type skin hypersensitivity, low T cell number and impaired lymphocyte proliferation to phytohaemagglutinin and concanavalin A. He had high normal serum immunoglobulin (Ig)G and IgA with low IgM and isohaemagglutinin. He presented with hypertensive encephalopathy at 5.5 years of age and an aortogram demonstrated abdominal aortic aneurysm with bilateral stenosis of renal arteries resulting in renovascular hypertension. His hypertension was difficult to control medically and autotransplant of his kidneys to the iliac arteries was performed, but he died in the immediate postoperative period. The relationship between immunodeficiency and collagen-vascular disease was discussed.
Authors:
Y L Lau; S N Wong; W M Lawton
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of paediatrics and child health     Volume:  28     ISSN:  1034-4810     ISO Abbreviation:  J Paediatr Child Health     Publication Date:  1992 Oct 
Date Detail:
Created Date:  1992-11-25     Completed Date:  1992-11-25     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  9005421     Medline TA:  J Paediatr Child Health     Country:  AUSTRALIA    
Other Details:
Languages:  eng     Pagination:  407-9     Citation Subset:  IM    
Affiliation:
Department of Paediatrics, University of Hong Kong.
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Humans
Male
Takayasu Arteritis / complications*,  immunology
Wiskott-Aldrich Syndrome / complications*,  immunology

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