Document Detail


Systemic light chain amyloidosis and Sjogren syndrome: an uncommon association.
MedLine Citation:
PMID:  19636991     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Sjogren syndrome is associated with lymphoproliferative disease in 7% of cases; however, association with AL amyloidosis is uncommon. We present a patient who presented simultaneously with Sjogren syndrome (supported by dry mouth, positive Schirmer's test, anti-Ro/SSA antibodies, and a lower lip salivary gland biopsy) and AL amyloidosis revealed by heart failure without myeloma. Although is it know that amyloidosis can masquerade as Sjogren syndrome, the occurrence of simultaneous AL amyloidosis and primary Sjogren syndrome has been reported rarely.
Authors:
Antoinette Perlat; Olivier Decaux; Renaud Gervais; Nathalie Rioux; Bernard Grosbois
Publication Detail:
Type:  Case Reports; Letter    
Journal Detail:
Title:  Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis     Volume:  16     ISSN:  1744-2818     ISO Abbreviation:  Amyloid     Publication Date:  2009  
Date Detail:
Created Date:  2010-06-11     Completed Date:  2010-09-07     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9433802     Medline TA:  Amyloid     Country:  England    
Other Details:
Languages:  eng     Pagination:  181-2     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Aged
Amyloidosis* / blood,  immunology,  pathology
Antibodies / blood,  immunology
Fatal Outcome
Female
Humans
Immunoglobulin Light Chains / blood*
Sjogren's Syndrome* / blood,  immunology,  pathology
Chemical
Reg. No./Substance:
0/Antibodies; 0/Immunoglobulin Light Chains

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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