Document Detail


Syndrome identification based on 2D analysis software.
MedLine Citation:
PMID:  16773127     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Clinical evaluation of children with developmental delay continues to present a challenge to the clinicians. In many cases, the face provides important information to diagnose a condition. However, database support with respect to facial traits is limited at present. Computer-based analyses of 2D and 3D representations of faces have been developed, but it is unclear how well a larger number of conditions can be handled by such systems. We have therefore analysed 2D pictures of patients each being affected with one of 10 syndromes (fragile X syndrome; Cornelia de Lange syndrome; Williams-Beuren syndrome; Prader-Willi syndrome; Mucopolysaccharidosis type III; Cri-du-chat syndrome; Smith-Lemli-Opitz syndrome; Sotos syndrome; Microdeletion 22q11.2; Noonan syndrome). We can show that a classification accuracy of >75% can be achieved for a computer-based diagnosis among the 10 syndromes, which is about the same accuracy achieved for five syndromes in a previous study. Pairwise discrimination of syndromes ranges from 80 to 99%. Furthermore, we can demonstrate that the criteria used by the computer decisions match clinical observations in many cases. These findings indicate that computer-based picture analysis might be a helpful addition to existing database systems, which are meant to assist in syndrome diagnosis, especially as data acquisition is straightforward and involves off-the-shelf digital camera equipment.
Authors:
Stefan Boehringer; Tobias Vollmar; Christiane Tasse; Rolf P Wurtz; Gabriele Gillessen-Kaesbach; Bernhard Horsthemke; Dagmar Wieczorek
Related Documents :
16199237 - Foreign accent syndrome: an organic disorder?
17665027 - Poems (polyneuropathy, organomegaly, endocrinopathy, m protein, skin lesions) syndrome:...
20497577 - Therapeutic approach to gradenigo's syndrome: a case report.
17581327 - Kasabach-merritt syndrome caused by giant hemangiomas of the spleen in patients with pr...
3354597 - Congenital scalp skull defects with distal limb anomalies (adams-oliver syndrome--mckus...
8275577 - Bilateral vocal cord paralysis in williams syndrome.
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't     Date:  2006-06-14
Journal Detail:
Title:  European journal of human genetics : EJHG     Volume:  14     ISSN:  1018-4813     ISO Abbreviation:  Eur. J. Hum. Genet.     Publication Date:  2006 Oct 
Date Detail:
Created Date:  2006-09-26     Completed Date:  2006-11-02     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  9302235     Medline TA:  Eur J Hum Genet     Country:  England    
Other Details:
Languages:  eng     Pagination:  1082-9     Citation Subset:  IM    
Affiliation:
Institut für Humangenetik, Universitätsklinikum Essen, Essen, Germany. correspondence@s-boehringer.org
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Child
Child, Preschool
Craniofacial Abnormalities / diagnosis
Diagnosis, Computer-Assisted / methods*
Facies*
Female
Humans
Infant
Male
Pattern Recognition, Automated*
Reproducibility of Results
Software*
Syndrome*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  TBP as a candidate gene for mental retardation in patients with subtelomeric 6q deletions.
Next Document:  A novel missense mutation in ACTG1 causes dominant deafness in a Norwegian DFNA20/26 family, but ACT...