Document Detail


Syndrome of hajdu-cheney: three case reports of orofacial interest.
MedLine Citation:
PMID:  20500061     Owner:  NLM     Status:  In-Data-Review    
Abstract/OtherAbstract:
Abstract Hajdu-Cheney syndrome is a rare, probably autosomal dominant connective tissue disorder with a variable expressivity. It is characterized by an osteoporotic skeleton, acro-osteolysis, a proportionate short stature, and distinctive orofacial anomalies. The aim of this article is to focus on the orofacial manifestations in two sporadic cases and one familial case with Hajdu-Cheney syndrome. Several common dental and craniofacial features are described. In contrast to earlier proposed diagnostic features, these patients show persisting deciduous teeth, problematic tooth eruption, and tendency toward a Class III malocclusion.
Authors:
E Vingerhoedt; I Bailleul-Forestier; P Fellus; J Schoenaers; J-P Frijns; C Carels
Publication Detail:
Type:  Journal Article     Date:  2010-03-01
Journal Detail:
Title:  The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association     Volume:  47     ISSN:  1545-1569     ISO Abbreviation:  Cleft Palate Craniofac. J.     Publication Date:  2010 Nov 
Date Detail:
Created Date:  2010-11-02     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9102566     Medline TA:  Cleft Palate Craniofac J     Country:  United States    
Other Details:
Languages:  eng     Pagination:  645-53     Citation Subset:  D; IM    
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