Document Detail


Surgical management of nonmultiple endocrine neoplasia endocrinopathies: state-of-the-art review.
MedLine Citation:
PMID:  19836485     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The development of genetic testing has given patients with familial endocrine diseases the opportunity to be identified earlier in life. The importance of this technological advancement cannot be underestimated, as some of these heritable diseases have significant potential for malignancy. This article focuses on the identification and surgical management of familial endocrinopathies of the thyroid, parathyroid, adrenal glands, and pancreas. Familial endocrinopathies discussed include hereditary nonmedullary carcinoma of the thyroid, Cowden disease, familial adenomatous polyposis, Carney complex, Werner syndrome, familial medullary thyroid carcinoma, Pendred syndrome, hereditary hyperparathyroidism jaw-tumor syndrome, familial isolated hyperparathyroidism, Beckwith- Wiedemann syndrome, Li-Fraumeni syndrome, neurofibromatosis I, von Hippel-Lindau disease, and tuberous sclerosis.
Authors:
Christine S Landry; Steven G Waguespack; Nancy D Perrier
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Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  The Surgical clinics of North America     Volume:  89     ISSN:  1558-3171     ISO Abbreviation:  Surg. Clin. North Am.     Publication Date:  2009 Oct 
Date Detail:
Created Date:  2009-10-19     Completed Date:  2009-12-03     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0074243     Medline TA:  Surg Clin North Am     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1069-89     Citation Subset:  AIM; IM    
Affiliation:
Department of Surgical Oncology, Unit 444, The University of Texas M. D. Anderson Cancer Center, Houston, TX 77030, USA.
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MeSH Terms
Descriptor/Qualifier:
Endocrine Gland Neoplasms / genetics,  surgery*
Endocrine Surgical Procedures / methods*
Genetic Testing
Humans
Neoplastic Syndromes, Hereditary / genetics,  surgery*

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