| Surgery for congenital conductive deafness in Klippel-Feil syndrome. | |
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MedLine Citation:
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PMID: 3408109 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A wide variety of anomalies of the middle and inner ear has been reported in association with congenital deafness in Klippel-Feil syndrome. Findings of six new exploratory tympanotomies are added to a review of 14 previously reported; for this entire group, better hearing was achieved in eight ears. When the only anomaly is a disconnection of the incudostapedial joint, good results can be expected from reconstruction of the ossicular chain. With the addition of the six newly reported stapedectomies, the success rate for this procedure now equals 50%. None of the fenestrations of the promontory performed for absence of the stapes and oval window have been successful. Since these results are encouraging, it is concluded that an exploratory tympanotomy should be considered during the course of hearing rehabilitation in cases of Klippel-Feil syndrome and a significant conductive hearing loss. Anomalies of inner ear structures established preoperatively may be a contraindication for stapedectomy. |
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Authors:
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P M van Rijn; C W Cremers |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The Annals of otology, rhinology, and laryngology Volume: 97 ISSN: 0003-4894 ISO Abbreviation: Ann. Otol. Rhinol. Laryngol. Publication Date: 1988 Jul-Aug |
Date Detail:
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Created Date: 1988-09-09 Completed Date: 1988-09-09 Revised Date: 2006-05-15 |
Medline Journal Info:
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Nlm Unique ID: 0407300 Medline TA: Ann Otol Rhinol Laryngol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 347-52 Citation Subset: AIM; IM |
Affiliation:
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Department of Otorhinolaryngology, St Radboud Hospital, University of Nijmegen, The Netherlands. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Female Fenestration, Labyrinth Hearing Loss / congenital* Hearing Loss, Conductive / congenital*, surgery Humans Klippel-Feil Syndrome / complications* Male Middle Aged Ossicular Prosthesis Stapes Surgery |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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