Document Detail


Sudden cardiac death under anesthesia in pediatric patient with Williams syndrome: a case report and review of literature.
MedLine Citation:
PMID:  20075535     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Williams syndrome is a complex syndrome characterized by developmental abnormalities, craniofacial dysmorphic features, and cardiac anomalies. Sudden death has been described as a very common complication associated with anesthesia, surgery, and procedures in this population. Anatomical abnormalities associated with the heart pre-dispose these individuals to sudden death. In addition to a sudden and rapid downhill course, lack of response to resuscitation is another significant feature seen in these patients. The authors report a five-year-old male with Williams syndrome, hypothyroidism, and attention deficit hyperactivity disorder. He suffered an anaphylactic reaction during CT imaging with contrast. Resuscitation was unsuccessful. Previous reports regarding the anesthetic management of patients with Williams are reviewed and the potential for sudden death or peri-procedure related cardiac arrest discussed in this report. The authors also review reasons for refractoriness to defined resuscitation guidelines in this patient population.
Authors:
Punkaj Gupta; Joseph D Tobias; Sunali Goyal; Martin D Miller; Elliot Melendez; Natan Noviski; Michael M De Moor; Vipin Mehta
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Annals of cardiac anaesthesia     Volume:  13     ISSN:  0974-5181     ISO Abbreviation:  Ann Card Anaesth     Publication Date:    2010 Jan-Apr
Date Detail:
Created Date:  2010-01-15     Completed Date:  2010-02-23     Revised Date:  2010-09-15    
Medline Journal Info:
Nlm Unique ID:  9815987     Medline TA:  Ann Card Anaesth     Country:  India    
Other Details:
Languages:  eng     Pagination:  44-8     Citation Subset:  IM    
Affiliation:
Division of Pediatric Critical Care, Massachusetts General Hospital, Harvard Medical School, Boston, MA 02114, USA. pgupta3@partners.org
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MeSH Terms
Descriptor/Qualifier:
Anesthesia / adverse effects*
Aortic Stenosis, Supravalvular / surgery*
Child, Preschool
Death, Sudden, Cardiac / etiology*
Electrocardiography
Humans
Male
Tomography, X-Ray Computed
Williams Syndrome / complications*
Comments/Corrections
Comment In:
Ann Card Anaesth. 2010 Sep-Dec;13(3):269   [PMID:  20826980 ]
Ann Card Anaesth. 2010 Sep-Dec;13(3):265-6   [PMID:  20826975 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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