Document Detail


Successful pregnancy in a patient with severe 11-beta-hydroxylase deficiency and novel mutations in CYP11B1 gene.
MedLine Citation:
PMID:  17726333     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
11 beta-Hydroxylase deficiency is a rare form of congenital adrenal hyperplasia, resulting in virilization, glucocorticoid deficiency and hypertension. There have been no previous reports in the literature of a successful pregnancy in a severely affected female. We report the first successful pregnancy resulting in a live birth for a female with 11 beta-hydroxylase deficiency and outline management issues from preconception to successful birth. We also report 2 novel mutations in the CYP11B1 gene leading to 11 beta-hydroxylase deficiency.
Authors:
Peter J Simm; Margaret R Zacharin
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Publication Detail:
Type:  Journal Article     Date:  2007-08-27
Journal Detail:
Title:  Hormone research     Volume:  68     ISSN:  1423-0046     ISO Abbreviation:  Horm. Res.     Publication Date:  2007  
Date Detail:
Created Date:  2007-11-06     Completed Date:  2007-12-13     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0366126     Medline TA:  Horm Res     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  294-7     Citation Subset:  IM    
Copyright Information:
(c) 2007 S. Karger AG, Basel.
Affiliation:
Department of Endocrinology and Diabetes, Royal Children's Hospital Melbourne, Australia. peter.simm@rch.org.au
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MeSH Terms
Descriptor/Qualifier:
Adrenal Hyperplasia, Congenital / genetics*
Adult
Female
Humans
Infertility, Female / genetics*
Mutation
Postpartum Period
Pregnancy
Pregnancy Complications / genetics*
Pregnancy Outcome*
Severity of Illness Index
Steroid 11-beta-Hydroxylase / genetics*
Chemical
Reg. No./Substance:
EC 1.14.15.4/Steroid 11-beta-Hydroxylase
Comments/Corrections
Comment In:
Horm Res. 2007;68(6):298-9   [PMID:  17726334 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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