Document Detail


Subclinical cardiological involvement in Sicilian patients with pure congenital muscular dystrophy.
MedLine Citation:
PMID:  16205611     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
AIM: Congenital muscular dystrophies (CMD) are a heterogeneous group of diseases characterized by a marked weakness, generalized hypotonia, joint contractures and a muscle biopsy suggestive of dystrophic changes. The aim of this study has been to assess the prevalence of heart involvement in merosin-positive CMD patients examined by echocardiography and Doppler. METHODS: A total of 10 merosin-positive CMD patients and 100 healthy children were evaluated by echocardiography and Doppler examinations and the results were compared. RESULTS: Three out of 10 patients showed a reduction of the ejection fraction and of the shortening fraction; in 1 case, a dilatation of left ventricular diastolic diameter was observed. CONCLUSIONS: In the 10 patients examined by echocardiography and Doppler, a heart involvement has been observed in 25% of cases.
Authors:
R Falsaperla; G Romeo; C Mattia; P Pavone; S Quattrocchi
Publication Detail:
Type:  Comparative Study; Journal Article    
Journal Detail:
Title:  Minerva pediatrica     Volume:  57     ISSN:  0026-4946     ISO Abbreviation:  Minerva Pediatr.     Publication Date:  2005 Oct 
Date Detail:
Created Date:  2005-10-05     Completed Date:  2005-12-19     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0400740     Medline TA:  Minerva Pediatr     Country:  Italy    
Other Details:
Languages:  eng     Pagination:  275-9     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, University of Catania, Catania, Italy. raffaelefalsaperla@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Child
Child, Preschool
Data Interpretation, Statistical
Diastole
Echocardiography, Doppler
Female
Heart Diseases / diagnosis,  epidemiology,  etiology*
Humans
Infant
Italy
Male
Muscular Dystrophies / complications*,  congenital*
Prevalence
Stroke Volume
Ultrasonography, Doppler, Color

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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