Document Detail


Sturge-Weber syndrome with no leptomeningeal enhancement on MRI.
MedLine Citation:
PMID:  9561524     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome characterized by a facial nevus flammeus associated with seizures, developmental delay, and, often, with hemiparesis and hemianopia. On MRI, the most characteristic finding has been reported to be leptomeningeal enhancement, believed to represent leakage of contrast medium through the anomalous pial vessels that characterize the disease. We present a case of SWS with no evidence of leptomeningeal enhancement. This case illustrates that leptomeningeal enhancement need not be present in SWS, and the absence of this characteristic finding does not preclude the diagnosis.
Authors:
N J Fischbein; A J Barkovich; Y Wu; B O Berg
Related Documents :
10327144 - Prenatal sonographic appearances of klippel-trenaunay-weber syndrome.
17222124 - Avellis syndrome due to borreliosis.
2702334 - Alexia with agraphia.
18639044 - Acute cervical cord injury complicating klippel-feil deformity and mimicking 'man in th...
18573354 - The antiphospholipid syndrome and infections in a child with trisomy 21.
6437074 - The smith-lemli-opitz syndrome. a detailed pathological study as a clue to a etiologica...
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Neuroradiology     Volume:  40     ISSN:  0028-3940     ISO Abbreviation:  Neuroradiology     Publication Date:  1998 Mar 
Date Detail:
Created Date:  1998-06-19     Completed Date:  1998-06-19     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  1302751     Medline TA:  Neuroradiology     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  177-80     Citation Subset:  IM    
Affiliation:
Nancy.Fischbein@radiology.ucsf.edu
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adolescent
Arachnoid / pathology*
Humans
Magnetic Resonance Imaging
Male
Pia Mater / pathology*
Sturge-Weber Syndrome / pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  MRI-neuropathological correlations in type 1 lissencephaly.
Next Document:  Magnetic resonance signal intensity and volume changes after endovascular treatment of intracranial ...