Document Detail


Sturge-Weber syndrome variant with atypical intracranial findings: case report.
MedLine Citation:
PMID:  16566882     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Sturge-Weber syndrome is characterized by a facial port-wine nevus, leptomeningeal angiomatosis, and glaucoma; it is commonly complicated by epilepsy and hemiparesis. We present a patient with a head and neck port-wine nevus, glaucoma, abnormalities of the intracranial deep veins, and untreated communicating hydrocephalus. The patient lacks any radiologic or clinical evidence of cerebral leptomeningeal angiomatosis. Considering that intracranial venous anomalies also are likely compatible with the embryologic explanation of Sturge-Weber syndrome, this child can serve as an unusual example of Sturge-Weber syndrome type II.
Authors:
Anil V Yallapragada; Joel K Cure; Kenton R Holden
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of child neurology     Volume:  21     ISSN:  0883-0738     ISO Abbreviation:  J. Child Neurol.     Publication Date:  2006 Feb 
Date Detail:
Created Date:  2006-03-28     Completed Date:  2006-09-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8606714     Medline TA:  J Child Neurol     Country:  Canada    
Other Details:
Languages:  eng     Pagination:  155-7     Citation Subset:  IM    
Affiliation:
Department of Neurosciences, Medical University of South Carolina, Charleston, USA.
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MeSH Terms
Descriptor/Qualifier:
Cephalometry
Cerebral Angiography
Cerebral Veins / abnormalities*,  pathology
Child
Cranial Sinuses / abnormalities,  surgery
Follow-Up Studies
Glaucoma / diagnosis*
Humans
Hydrocephalus / diagnosis*
Intracranial Arteriovenous Malformations / diagnosis*
Magnetic Resonance Angiography
Magnetic Resonance Imaging
Male
Orbit / blood supply
Sturge-Weber Syndrome / diagnosis*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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