Document Detail


Studies of cellular hypersensitivity to ionising radiation in Friedreich's ataxia.
MedLine Citation:
PMID:  7161608     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Skin fibroblasts from seven patients with Friedreich's ataxia showed a small but significant increase in sensitivity to ionising radiation, as measured by post-irradiation clonal growth, when compared with cells from ten age-matched control subjects and from eight patients with motor neuron disease. Fibroblasts from three patients with Friedreich's ataxia also showed impairment of their ability to repair potentially lethal damage after ionising radiation. These findings are consistent with the view that defective DNA reparative mechanisms may be involved in the pathogenesis of Friedreich's ataxia.
Authors:
S Chamberlain; P D Lewis
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Journal of neurology, neurosurgery, and psychiatry     Volume:  45     ISSN:  0022-3050     ISO Abbreviation:  J. Neurol. Neurosurg. Psychiatr.     Publication Date:  1982 Dec 
Date Detail:
Created Date:  1983-04-15     Completed Date:  1983-04-15     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  2985191R     Medline TA:  J Neurol Neurosurg Psychiatry     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  1136-8     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Clone Cells
DNA Repair / radiation effects*
Dose-Response Relationship, Radiation
Female
Fibroblasts / radiation effects
Friedreich Ataxia / metabolism*
Humans
Male
Mitosis / radiation effects*
Comments/Corrections

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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