Document Detail


Stroke in early childhood due to homocystinuria.
MedLine Citation:
PMID:  20837312     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A previously healthy girl, age 3 years 9 months, presented with right-sided hemiparesis and seizures. Ischemic infarction was confirmed through magnetic resonance imaging and magnetic resonance angiography. Extensive evaluation to discover the underlying etiologies and risk factors predisposing this patient to stroke included coagulation defects, cardiac anomalies, congenital inborn metabolism deficiency, and infections and trauma. Based on the clinical and laboratory results, a diagnosis of homocystinuria was made. Homocystinuria is an inherited disorder that affects the metabolism of the amino acid methionine. Although homocystinuria is usually associated with ischemic strokes, the sudden onset of stroke as the initial clinical presentation of homocystinuria is very rare in early childhood. Based on this case, however, metabolic screening for hyperhomocystinemia is recommended in any child presenting with a stroke.
Authors:
Füsun Alehan; Semra Saygi; Sansal Gedik; Esra Meltem Kayahan Ulu
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  43     ISSN:  1873-5150     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2010 Oct 
Date Detail:
Created Date:  2010-09-14     Completed Date:  2011-01-21     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  294-6     Citation Subset:  IM    
Copyright Information:
Copyright © 2010 Elsevier Inc. All rights reserved.
Affiliation:
Division of Child Neurology, Baskent University Faculty of Medicine, Ankara, Turkey.
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MeSH Terms
Descriptor/Qualifier:
Brain Ischemia / etiology,  pathology
Cerebral Angiography
Child, Preschool
Female
Homocystinuria / complications*,  pathology
Humans
Magnetic Resonance Imaging
Paresis / etiology*,  pathology
Seizures / etiology*,  pathology
Stroke / etiology*,  pathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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