Document Detail


Stiff-man syndrome updated.
MedLine Citation:
PMID:  2664359     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Stiff-man syndrome, a rare disorder characterized by intermittent spasms and stiffness of the axial muscles, is associated with an electromyographic pattern of continuous motor unit activity in affected muscles. Since the initial description in 1956, the stiff-man syndrome has been reported to occur in various clinical and neurologic settings. In this study, we reviewed the current state of knowledge about this syndrome, defined diagnostic criteria, provided a long-term follow-up of the disorder, and assessed rehabilitative attempts in affected patients. Use of rigorous criteria that identify patients who have the stiff-man syndrome is important because the initial clinical manifestations are similar to those of other neuromuscular diseases. Analysis of 13 patients with stiff-man syndrome examined at the Mayo Clinic during the past 30 years revealed that treatment with diazepam decreased the muscle spasms. Because some muscle spasms usually persist, rehabilitation is an important adjunct that may further improve function when it is centered on the treatment of low-back pain and hyperlordosis, mobility problems, gait abnormalities, and muscular stiffness.
Authors:
T R Lorish; G Thorsteinsson; F M Howard
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Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  Mayo Clinic proceedings. Mayo Clinic     Volume:  64     ISSN:  0025-6196     ISO Abbreviation:  Mayo Clin. Proc.     Publication Date:  1989 Jun 
Date Detail:
Created Date:  1989-08-17     Completed Date:  1989-08-17     Revised Date:  2007-10-29    
Medline Journal Info:
Nlm Unique ID:  0405543     Medline TA:  Mayo Clin Proc     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  629-36     Citation Subset:  AIM; IM    
Affiliation:
Department of Physical Medicine and Rehabilitation, Mayo Clinic, Rochester, MN 55905.
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MeSH Terms
Descriptor/Qualifier:
Adult
Diagnosis, Differential
Diazepam / therapeutic use
Electromyography
Female
Gait
Humans
Lordosis / complications*
Male
Middle Aged
Muscle Spasticity / complications*,  diagnosis,  drug therapy
Neuromuscular Diseases / diagnosis
Spasm / complications
Syndrome
Chemical
Reg. No./Substance:
439-14-5/Diazepam

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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