| Splenic vascular malformations and portal hypertension in hereditary hemorrhagic telangiectasia: sonographic findings. | |
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MedLine Citation:
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PMID: 11180187 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Hereditary hemorrhagic telangiectasia, or Osler-Rendu-Weber disease, is an autosomal dominant disorder in which a variety of vascular dysplasias occur throughout the organ systems. We report the gray-scale and color Doppler sonographic findings in a case of hereditary hemorrhagic telangiectasia. Gray-scale sonographic examination revealed massive splenomegaly, multiple dilated intrasplenic vascular structures (some with adjacent punctate calcifications), an aneurysmal dilatation of the splenic vein, dilated intrahepatic portal branches, and marked atrophy of the right hepatic lobe. Color Doppler sonography showed dilatation of the truncus coeliacus and high-velocity flow in the splenic artery. There were significant aliasing in the splenic hilum and an abnormal, arterialized flow in intrasplenic branches of the splenic vein. The splenic vein was massively enlarged with increased flow velocity and contained an isolated aneurysmal dilatation in the hilum. There were multiple serpiginous retroperitoneal collateral vessels, and the left gastric vein was dilated with hepatofugal flow. The patient had portal hypertension that developed secondary to the increased portal flow. |
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Authors:
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M Seçil; A Göktay; O Dicle; T Pirnar |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Journal of clinical ultrasound : JCU Volume: 29 ISSN: 0091-2751 ISO Abbreviation: J Clin Ultrasound Publication Date: 2001 Jan |
Date Detail:
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Created Date: 2001-02-22 Completed Date: 2001-04-12 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0401663 Medline TA: J Clin Ultrasound Country: United States |
Other Details:
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Languages: eng Pagination: 56-9 Citation Subset: IM |
Copyright Information:
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Copyright 2000 John Wiley & Sons, Inc. |
Affiliation:
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Department of Radiology, Dokuz Eylül University Hospital, Inciralti, 35340 Izmir, Turkey. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Aneurysm / etiology, pathology, ultrasonography* Humans Hypertension, Portal / etiology* Male Regional Blood Flow Splenic Artery / pathology, ultrasonography Splenic Vein / pathology*, ultrasonography Splenomegaly / ultrasonography Telangiectasia, Hereditary Hemorrhagic / complications*, ultrasonography* Ultrasonography, Doppler, Color |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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