| Spindle cell hemangioendotheliomas associated with multiple skeletal enchondromas: a variant of Maffucci's syndrome. | |
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MedLine Citation:
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PMID: 9653917 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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An unusual case of Maffucci's syndrome confined to an extremity with an additional superficial lymphangioma in the same limb is described. The patient, a 47-year-old woman, presented with several painful subcutaneous spindle cell hemangioendotheliomas (SCHs) and multiple lytic bone lesions, some calcified, in the left leg. She has been followed for two years and continues to do well. The combination of SCHs and multiple enchondromas (ENCHs) should be searched in any patient who presents with SCHs or multiple ENCHs, because there is a significant risk of malignant transformation. |
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Authors:
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S Yáñez; J F Val-Bernal; C Mira; M A Echevarría; M C González-Vela; F Arce |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: General & diagnostic pathology Volume: 143 ISSN: 0947-823X ISO Abbreviation: Gen Diagn Pathol Publication Date: 1998 Apr |
Date Detail:
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Created Date: 1998-09-09 Completed Date: 1998-09-09 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9511700 Medline TA: Gen Diagn Pathol Country: GERMANY |
Other Details:
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Languages: eng Pagination: 331-5 Citation Subset: IM |
Affiliation:
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Department of Dermatology, Marqués de Valdecilla University Hospital, Medical Faculty, University of Cantabria, Santander, Spain. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Bone Neoplasms
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complications*,
pathology,
radiography Enchondromatosis / complications*, pathology, radiography Female Hemangioendothelioma / complications*, pathology Humans Middle Aged |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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