Document Detail

Spinal stenosis with paraparesis in albright hereditary osteodystrophy. Case report and review of the literature.
MedLine Citation:
PMID:  18552518     Owner:  NLM     Status:  MEDLINE    
We describe thoracic spinal stenosis with progressive myelopathy in association with Albright hereditary osteodystrophy (AHO) in a 12-year-old child with delayed diagnosis and review the relevant literature in order to identify the pathophysiological mechanism. The child was successfully treated by decompressive upper thoracic laminoplasty with full neurological recovery. The pathological changes of the skin also dissolved. Ten more cases of myelopathy and paraparesis in association with AHO, of whom two were children, could be found in the literature. Basically, two different causes for the spinal canal stenosis could be identified: abnormal ossifications of ligaments and congenital narrow spinal canal due to short vertebral pedicles. Awareness of structural spinal column changes in AHO is essential in order to appreciate the neurological symptoms of a beginning myelopathy before irreversible damage to the myelum occurs.
Erik J van Lindert; Ronald H M A Bartels; Kees Noordam
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Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2008-06-13
Journal Detail:
Title:  Pediatric neurosurgery     Volume:  44     ISSN:  1423-0305     ISO Abbreviation:  Pediatr Neurosurg     Publication Date:  2008  
Date Detail:
Created Date:  2008-07-02     Completed Date:  2008-09-09     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9114967     Medline TA:  Pediatr Neurosurg     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  337-40     Citation Subset:  IM    
Copyright Information:
2008 S. Karger AG, Basel
Department of Neurosurgery, Radboud University Nijmegen Medical Center, Nijmegen, The Netherlands.
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MeSH Terms
Fibrous Dysplasia, Polyostotic / complications*,  genetics
Paraparesis / etiology*
Spinal Stenosis / etiology*

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