| Spinal cheiro-oral syndrome: a common neurological entity in an unusual site. | |
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MedLine Citation:
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PMID: 22212989 Owner: NLM Status: Publisher |
Abstract/OtherAbstract:
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Background and purpose : Cheiro-oral syndrome (COS) is an established neurological entity characterized by a sensory impairment confined to the mouth angle and ipsilateral finger(s)/ hand. The current understanding of localization is a concomitant involvement of the spinothalamic and tri-geminothalamic tract between the cortex and pons. The cervical spinal cord has not been mentioned in this situation yet, and this unusual location may heretofore increase the risk of misdiagnosis. Material and methods : Six patients who presented with unilateral COS due to cervical cord disorder are reported. Results : All patients were women and their age ranged between 42 and 70 years. Their neurological deficits included unila-teral paraesthesiae restricted to cheiro-oral distribution, posi-tive radicular sign, and mild change of tendon reflex. Cervical spinal stenosis at middle/lower cervical spine with variable magnitude of cord compression and intrinsic cord damage was found. A diagnostic dilemma obviously arises from the lack of tangible neurological signs or typical pattern of myelopathy, in addition to the previous concept of cerebral involvement. A benign course ensued in all reported patients. Conclusions: Cheiro-oral syndrome can be an early neurological sign for cervical cord disorder; it further suggests that it is a strong neurological but weak localizing sign. A reciprocal influence of multiple factors is considered to generate COS at the cervical cord. Therefore, an absence of brain pathology should lead to a thorough examination of the cervical cord in case of COS. |
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Authors:
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Hung-Sheng Lin; Hsin-Ling Yin; Chi Chui; Chun-Chung Lui; Wei-Hsi Chen |
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Publication Detail:
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Type: JOURNAL ARTICLE |
Journal Detail:
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Title: Neurologia i neurochirurgia polska Volume: 45 ISSN: 0028-3843 ISO Abbreviation: - Publication Date: 2011 |
Date Detail:
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Created Date: 2012-1-3 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0101265 Medline TA: Neurol Neurochir Pol Country: - |
Other Details:
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Languages: ENG Pagination: 583-589 Citation Subset: - |
Affiliation:
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Dr. Wei-Hsi Chen, Department of Neurology, Chang Gung Memorial Hospital - Kaohsiung Medical Center, 123 Tai Pei Road, Niao Sung District, Kaohsiung City 833, Taiwan, phone 886 7 7317123, e-mail: brainhemostasis@yahoo.com. |
Vernacular Title:
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Rdzeniowy zespół twarzowo-palcowy: częsty zespół w nietypowej lokalizacji. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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