Document Detail

Spinal cheiro-oral syndrome: a common neurological entity in an unusual site.
MedLine Citation:
PMID:  22212989     Owner:  NLM     Status:  MEDLINE    
BACKGROUND AND PURPOSE: Cheiro-oral syndrome (COS) is an established neurological entity characterized by a sensory impairment confined to the mouth angle and ipsilateral finger(s)/ hand. The current understanding of localization is a concomitant involvement of the spinothalamic and trigeminothalamic tract between the cortex and pons. The cervical spinal cord has not been mentioned in this situation yet, and this unusual location may heretofore increase the risk of misdiagnosis.
MATERIAL AND METHODS: Six patients who presented with unilateral COS due to cervical cord disorder are reported.
RESULTS: All patients were women and their age ranged between 42 and 70 years. Their neurological deficits included unilateral paraesthesiae restricted to cheirooral distribution, positive radicular sign, and mild change of tendon reflex. Cervical spinal stenosis at middle/lower cervical spine with variable magnitude of cord compression and intrinsic cord damage was found. A diagnostic dilemma obviously arises from the lack of tangible neurological signs or typical pattern of myelopathy, in addition to the previous concept of cerebral involvement. A benign course ensued in all reported patients.
CONCLUSIONS: Cheiro-oral syndrome can be an early neurological sign for cervical cord disorder; it further suggests that it is a strong neurological but weak localizing sign. A reciprocal influence of multiple factors is considered to generate COS at the cervical cord. Therefore, an absence of brain pathology should lead to a thorough examination of the cervical cord in case of COS.
Hung-Sheng Lin; Hsin-Ling Yin; Chi Chui; Chun-Chung Lui; Wei-Hsi Chen
Related Documents :
15745499 - Vesical hemangioma in patient with klippel-trenaunay-weber syndrome.
7792689 - Extradural tumor causing spinal cord compression in klippel-trenaunay-weber syndrome.
21879899 - Cord colitis syndrome in cord-blood stem-cell transplantation.
12590699 - Cobb syndrome in an infant: treatment with endovascular embolization and corticosteroid...
3408109 - Surgery for congenital conductive deafness in klippel-feil syndrome.
3422849 - Phacomatosis pigmentovascularis: a new syndrome? report of four cases.
5696209 - On the shape of the erythrocyte.
22707629 - Respiratory distress syndrome due to a novel homozygous abca3 mutation in a term neonate.
4094729 - The anterior segment anomalies in the warburg syndrome. a study of new cases.
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Neurologia i neurochirurgia polska     Volume:  45     ISSN:  0028-3843     ISO Abbreviation:  Neurol. Neurochir. Pol.     Publication Date:    2011 Nov-Dec
Date Detail:
Created Date:  2012-01-03     Completed Date:  2012-02-14     Revised Date:  2012-11-07    
Medline Journal Info:
Nlm Unique ID:  0101265     Medline TA:  Neurol Neurochir Pol     Country:  Poland    
Other Details:
Languages:  eng     Pagination:  583-9     Citation Subset:  IM    
Department of Neurology, Chang Gung Memorial Hospital - Kaohsiung Medical Center, Taiwan.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Cervical Vertebrae* / pathology
Fingers / abnormalities*
Middle Aged
Mouth Abnormalities / diagnosis*
Severity of Illness Index
Spinal Cord Diseases / diagnosis*,  pathology
Spinal Stenosis / diagnosis*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

Previous Document:  Surgical treatment of symptomatic vertebral haemangiomas.
Next Document:  [Deep brain stimulation in the treatment of torticollis and Meige syndrome].