Document Detail


Segregation and sporadic cases of Duchenne muscular dystrophy in the Henan Province, China.
MedLine Citation:
PMID:  2365377     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
In the Henan province, China, the segregation ratio of Duchenne muscular dystrophy, estimated through classical segregation analysis on 103 sibships, is p = 0.462, and the maximum likelihood proportion of sporadic cases is x = 0.264. These figures are in agreement with the results of segregation analysis on 1,800 families from different countries; also, the Henan population shows a slight segregation distortion and lacks a fraction of the sporadic cases predicted under mutation-selection equilibrium. Although not statistically significant, the downward departure of the estimated parameters from their expectations under the mendelian equilibrium hypothesis (p = 0.5; x = 0.333) confirms an anomalous segregation pattern for Duchenne muscular dystrophy. A possible role of germinal mosaicism in concealing a fraction of sporadic cases is discussed.
Authors:
W M Fu; G Barbujani
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Human heredity     Volume:  40     ISSN:  0001-5652     ISO Abbreviation:  Hum. Hered.     Publication Date:  1990  
Date Detail:
Created Date:  1990-08-13     Completed Date:  1990-08-13     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0200525     Medline TA:  Hum Hered     Country:  SWITZERLAND    
Other Details:
Languages:  eng     Pagination:  167-72     Citation Subset:  IM    
Affiliation:
Shanghai Medical University, People's Republic of China.
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MeSH Terms
Descriptor/Qualifier:
China / epidemiology
Gene Frequency
Genetics, Population
Humans
Likelihood Functions
Male
Muscular Dystrophies / genetics*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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