| Scimitar syndrome in an infant with right lung hypoplasia, ventricular septal defect, and severe pulmonary hypertension. | |
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MedLine Citation:
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PMID: 20941566 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 5-month-old boy was presented for surgical repair of scimitar syndrome associated with right lung hyperplasia, severe pulmonary hypertension, ventricular septal defect (VSD), and atrial septal defect. The calculated shunt fraction (Qp/Qs) was 3.1:1.0, pulmonary vascular resistance was 4.6, and the perfusion lung scan showed a marked decrease (11%) in right pulmonary blood flow. Surgical repair was performed through the right fourth intercostal space with the patient supine. The anomalous vein was divided and interposed with a short azygos vein graft, followed by closure of the VSD. Finally, the interposed azygos vein was anastomosed to the left atrium. Although pulmonary artery pressure was normalized at the 2-year follow-up, cardiac catheterization 6 months after the operation demonstrated right pulmonary vein obstruction. |
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Authors:
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Gen Shinohara; Kiyozo Morita; Yoshimasa Uno; Masahito Yamashiro; Kazuhiro Hashimoto |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2010-10-13 |
Journal Detail:
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Title: General thoracic and cardiovascular surgery Volume: 58 ISSN: 1863-6713 ISO Abbreviation: Gen Thorac Cardiovasc Surg Publication Date: 2010 Oct |
Date Detail:
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Created Date: 2010-10-13 Completed Date: 2011-02-02 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101303952 Medline TA: Gen Thorac Cardiovasc Surg Country: Japan |
Other Details:
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Languages: eng Pagination: 524-7 Citation Subset: IM |
Affiliation:
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Department of Cardiac Surgery, Jikei University School of Medicine, Minato-ku, Tokyo, Japan. genshino@iris.ocn.ne.jp |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Abnormalities, Multiple* Azygos Vein / transplantation Blood Pressure Heart Catheterization Heart Septal Defects, Atrial / complications, surgery Heart Septal Defects, Ventricular / complications*, physiopathology, surgery Humans Hypertension, Pulmonary / etiology*, physiopathology, surgery Infant Lung / abnormalities*, blood supply Male Perfusion Imaging Pulmonary Circulation Pulmonary Veno-Occlusive Disease / etiology Scimitar Syndrome / complications*, physiopathology, surgery Treatment Outcome Vascular Grafting / adverse effects Vascular Resistance |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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