Document Detail

Scimitar syndrome in an infant with right lung hypoplasia, ventricular septal defect, and severe pulmonary hypertension.
MedLine Citation:
PMID:  20941566     Owner:  NLM     Status:  MEDLINE    
A 5-month-old boy was presented for surgical repair of scimitar syndrome associated with right lung hyperplasia, severe pulmonary hypertension, ventricular septal defect (VSD), and atrial septal defect. The calculated shunt fraction (Qp/Qs) was 3.1:1.0, pulmonary vascular resistance was 4.6, and the perfusion lung scan showed a marked decrease (11%) in right pulmonary blood flow. Surgical repair was performed through the right fourth intercostal space with the patient supine. The anomalous vein was divided and interposed with a short azygos vein graft, followed by closure of the VSD. Finally, the interposed azygos vein was anastomosed to the left atrium. Although pulmonary artery pressure was normalized at the 2-year follow-up, cardiac catheterization 6 months after the operation demonstrated right pulmonary vein obstruction.
Gen Shinohara; Kiyozo Morita; Yoshimasa Uno; Masahito Yamashiro; Kazuhiro Hashimoto
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2010-10-13
Journal Detail:
Title:  General thoracic and cardiovascular surgery     Volume:  58     ISSN:  1863-6713     ISO Abbreviation:  Gen Thorac Cardiovasc Surg     Publication Date:  2010 Oct 
Date Detail:
Created Date:  2010-10-13     Completed Date:  2011-02-02     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101303952     Medline TA:  Gen Thorac Cardiovasc Surg     Country:  Japan    
Other Details:
Languages:  eng     Pagination:  524-7     Citation Subset:  IM    
Department of Cardiac Surgery, Jikei University School of Medicine, Minato-ku, Tokyo, Japan.
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MeSH Terms
Abnormalities, Multiple*
Azygos Vein / transplantation
Blood Pressure
Heart Catheterization
Heart Septal Defects, Atrial / complications,  surgery
Heart Septal Defects, Ventricular / complications*,  physiopathology,  surgery
Hypertension, Pulmonary / etiology*,  physiopathology,  surgery
Lung / abnormalities*,  blood supply
Perfusion Imaging
Pulmonary Circulation
Pulmonary Veno-Occlusive Disease / etiology
Scimitar Syndrome / complications*,  physiopathology,  surgery
Treatment Outcome
Vascular Grafting / adverse effects
Vascular Resistance

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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