Document Detail


Scapuloperoneal syndromes. Absence of linkage to the 4q35 FSHD locus.
MedLine Citation:
PMID:  7487558     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: To investigate whether two forms of the scapuloperoneal syndrome result from genetic defects allelic to facioscapulohumeral dystrophy (FSHD). DESIGN: Two kindreds with scapuloperoneal syndromes underwent clinical, histologic, and electrophysiologic evaluation followed by genetic evaluation with probes closely linked to FSHD. RESULTS: Although the proband in each kindred had facial, scapular stabilizer, and humeral weakness, raising the possibility of FSHD, evaluation of multiple other affected family members showed patterns of involvement that were clinically distinct from typical FSHD. In addition, DNA studies showed no linkage to the 4q35 FSHD locus in either kindred. CONCLUSION: We conclude that these two forms of the scapuloperoneal syndrome are genetically distinct from FSHD.
Authors:
R Tawil; G J Myers; B Weiffenbach; R C Griggs
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  Archives of neurology     Volume:  52     ISSN:  0003-9942     ISO Abbreviation:  Arch. Neurol.     Publication Date:  1995 Nov 
Date Detail:
Created Date:  1995-12-12     Completed Date:  1995-12-12     Revised Date:  2007-11-14    
Medline Journal Info:
Nlm Unique ID:  0372436     Medline TA:  Arch Neurol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  1069-72     Citation Subset:  AIM; IM    
Affiliation:
Department of Neurology, School of Medicine and Dentistry, University of Rochester (NY), USA.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Female
Genetic Markers
Humans
Humerus
Linkage (Genetics)*
Male
Middle Aged
Neuromuscular Diseases / genetics*,  pathology
Pedigree
Peroneal Nerve
Scapula
Grant Support
ID/Acronym/Agency:
M01RR00044/RR/NCRR NIH HHS; NS22099/NS/NINDS NIH HHS
Chemical
Reg. No./Substance:
0/Genetic Markers

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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