Document Detail

SAPHO syndrome with affection of the mandible: diagnosis, treatment, and review of literature.
MedLine Citation:
PMID:  20674419     Owner:  NLM     Status:  MEDLINE    
The synovitis, acne, pustulosis, hyperostosis, and osteitis (SAPHO) syndrome is a rare syndrome of unknown etiology. Involvement of the mandible is found in almost 10% of cases. In the literature, conservative treatment is recommended most often, because decortication and partial resection are found to be ineffective and of temporary profit. We report a case of SAPHO syndrome in a 44-year-old women with unilateral hyperostosis of the mandible and massive painful swelling of the surrounding soft tissues. Owing to facial disfiguration and pain, resection of the affected bone followed by immediate reconstruction with a microvascular iliac crest flap were performed. The aim of this paper was to present the necessity of surgical intervention in SAPHO syndrome of the mandible in cases of esthetic and functional limitation.
Wolfgang Zemann; Mauro Pau; Matthias Feichtinger; Barbara Ferra-Matschy; Hans Kaercher
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Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2010-07-31
Journal Detail:
Title:  Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics     Volume:  111     ISSN:  1528-395X     ISO Abbreviation:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Publication Date:  2011 Feb 
Date Detail:
Created Date:  2011-01-17     Completed Date:  2011-06-15     Revised Date:  2012-11-01    
Medline Journal Info:
Nlm Unique ID:  9508562     Medline TA:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Country:  United States    
Other Details:
Languages:  eng     Pagination:  190-5     Citation Subset:  D; IM    
Copyright Information:
Copyright © 2011 Mosby, Inc. All rights reserved.
Department of Oral and Maxillofacial Surgery, Medical University Graz, Graz, Austria.
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MeSH Terms
Acquired Hyperostosis Syndrome / complications*,  diagnosis,  surgery
Bone Transplantation
Facial Asymmetry / diagnosis,  etiology*,  surgery
Functional Laterality
Ilium / transplantation
Mandibular Diseases / diagnosis,  etiology*,  surgery
Surgical Flaps
Treatment Outcome
Comment In:
Oral Surg Oral Med Oral Pathol Oral Radiol. 2012 Sep;114(3):401-3; author reply 403   [PMID:  22819457 ]

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