Document Detail


Ruptured sinus of Valsalva aneurysm in a child with Down syndrome: a rare cardiac anomaly.
MedLine Citation:
PMID:  20980963     Owner:  NLM     Status:  In-Process    
Abstract/OtherAbstract:
BACKGROUND: As many as forty to fifty per cent of children with Down syndrome are born with a cardiac anomaly. Sinus of Valsalva aneurysm in this syndrome is extremely rare, only three previous reports, and of adult onset.
CASE REPORT: An asymptomatic 9 and a half year boy with Down syndrome presented with a cardiac murmur at routine examination. Clinical examination, transthoracic and transesopahageal echocardiography revealed the presence of a ruptured sinus of Valsalva aneurysm from the non - coronary sinus protruding into the right atrium. The child underwent successful surgical repair with full recovery.
CONCLUSIONS: This fourth case report of sinus of Valsalva aneurysm occurring in association with Down syndrome is the youngest to date. Physicians caring for Down syndrome patients ought to be aware of this late onset cardiac malformation. Serial echocardiographic assessment of the aortic sinus of Valsalva in these patients may offer early detection.
Authors:
Abraham Benatar; Tine Decraene; Arjen Feenstra
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Medical science monitor : international medical journal of experimental and clinical research     Volume:  16     ISSN:  1643-3750     ISO Abbreviation:  Med. Sci. Monit.     Publication Date:  2010 Nov 
Date Detail:
Created Date:  2010-10-28     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9609063     Medline TA:  Med Sci Monit     Country:  Poland    
Other Details:
Languages:  eng     Pagination:  CS135-7     Citation Subset:  IM    
Affiliation:
Department of Pediatric Cardiology, Unversitair Ziekenhuis Brussel, Free University of Brussels, Brussels, Belgium. Abraham.Benatar@uzbrussel.be
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