Document Detail


The role of prokineticins in the pathogenesis of hypogonadotropic hypogonadism.
MedLine Citation:
PMID:  20502053     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The prokineticin system comprises two multifunctional secreted proteins, prokineticin-1 (PROK1) and prokineticin-2 (PROK2), and their cognate G protein-coupled receptors. The prokineticins were originally identified as endogenous regulators of gastrointestinal motility. Currently, these bioactive peptides are involved in a wide spectrum of biological functions, including angiogenesis, neurogenesis, circadian rhythms, nociception, hematopoiesis and immune response. Mice homozygous for null mutations in Prokr2 or Prok2 recapitulate the human phenotype of Kallmann syndrome, exhibiting severe atrophy of the reproductive system and hypoplastic olfactory bulbs. Indeed, the evidence from several naturally inactivating mutations in the PROK2 and PROKR2 genes in patients with Kallmann syndrome and normosmic hypogonadotropic hypogonadism also indicate the essential role of PROK2 in olfactory bulb morphogenesis and GnRH secretion in humans.
Authors:
Ana Paula Abreu; Ursula B Kaiser; Ana Claudia Latronico
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review     Date:  2010-05-21
Journal Detail:
Title:  Neuroendocrinology     Volume:  91     ISSN:  1423-0194     ISO Abbreviation:  Neuroendocrinology     Publication Date:  2010  
Date Detail:
Created Date:  2010-07-14     Completed Date:  2010-11-04     Revised Date:  2011-07-19    
Medline Journal Info:
Nlm Unique ID:  0035665     Medline TA:  Neuroendocrinology     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  283-90     Citation Subset:  IM    
Copyright Information:
Copyright 2010 S. Karger AG, Basel.
Affiliation:
Unidade de Endocrinologia do Desenvolvimento, Laboratório de Hormônios e Genética Molecular, LIM/42, Hospital das Clínicas, Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brasil.
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MeSH Terms
Descriptor/Qualifier:
Animals
Female
Gastrointestinal Hormones / genetics*,  metabolism
Humans
Hypogonadism / genetics*,  metabolism
Male
Mice
Mutation
Neuropeptides / genetics*,  metabolism
Receptors, G-Protein-Coupled / genetics*,  metabolism
Receptors, Peptide / genetics*,  metabolism
Vascular Endothelial Growth Factor, Endocrine-Gland-Derived / genetics*,  metabolism
Grant Support
ID/Acronym/Agency:
U54 HD28138/HD/NICHD NIH HHS
Chemical
Reg. No./Substance:
0/Gastrointestinal Hormones; 0/Neuropeptides; 0/PROK2 protein, human; 0/PROKR1 protein, human; 0/PROKR2 protein, human; 0/Receptors, G-Protein-Coupled; 0/Receptors, Peptide; 0/Vascular Endothelial Growth Factor, Endocrine-Gland-Derived
Comments/Corrections

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