Document Detail

Right atrial rhabdomyoma acting as the substrate for Wolff-Parkinson-White syndrome in a 3-month-old infant.
MedLine Citation:
PMID:  16261787     Owner:  NLM     Status:  MEDLINE    
We report a 3-month-old infant girl who presented with supraventricular tachycardia, who was detected to have a large right atrial rhabdomyoma and evidence of Wolff-Parkinson-White (WPW) syndrome with an accessory pathway corresponding to the position of the tumour. In view of the resistant cardiac arrhythmia and large size of the tumour, the infant underwent surgical excision of the tumour. The evidence of WPW syndrome disappeared from the surface electrocardiogram immediately upon removal of the tumour. A second resolving tumour in the interventricular septum was also detected during the investigation. Although there are no other stigmata of tuberous sclerosis at present, our infant requires close follow-up. Right atrial rhabdomyomas are rare and to our knowledge this is the first reported instance where we could document clearly that the tumour itself formed the substrate for the WPW syndrome.
Poothirikovil Venugopalan; Jaya Suresh Babu; Ahmed Al-Bulushi
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Acta cardiologica     Volume:  60     ISSN:  0001-5385     ISO Abbreviation:  Acta Cardiol     Publication Date:  2005 Oct 
Date Detail:
Created Date:  2005-11-02     Completed Date:  2006-01-20     Revised Date:  2009-06-11    
Medline Journal Info:
Nlm Unique ID:  0370570     Medline TA:  Acta Cardiol     Country:  Belgium    
Other Details:
Languages:  eng     Pagination:  543-5     Citation Subset:  IM    
Department of Child Health, Sultan Qaboos University Hospital, Muscat, Sultanate of Oman.
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MeSH Terms
Diagnosis, Differential
Heart Atria / pathology
Heart Neoplasms* / diagnosis,  physiopathology,  surgery
Heart Septum / pathology
Heart Ventricles / pathology
Rhabdomyoma* / diagnosis,  physiopathology,  surgery
Tachycardia, Supraventricular / diagnosis
Wolff-Parkinson-White Syndrome* / diagnosis,  physiopathology,  surgery

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