Document Detail

Rhomb- and bickerstaff encephalitis: two clinical phenotypes?
MedLine Citation:
PMID:  23419478     Owner:  NLM     Status:  MEDLINE    
We report unusual cases of brainstem encephalitis in two young boys. Both presented with acute febrile illness, progressive encephalopathy, and marked cerebrospinal fluid pleocytosis. Case one shared some of the clinical features that have been seen in previously reported cases of brainstem encephalitis, such as ophthalmoplegia, ataxia, and progressive encephalopathy. Case two presented with similar clinical features, although without ophthalmoplegia and ataxia. A review of magnetic resonance imaging revealed mild differences with respect to anatomic lesion localization and confirmed a neuroanatomic basis for the variance in each patient's symptoms. The features of these cases deviate from the classical symptoms described in the Miller-Fisher syndrome/Bickerstaff brainstem encephalitis/Guillain-Barré syndrome spectrum, although the cause for variability in clinical phenotypes is unknown.
Rebecca C Gologorsky; Jerome A Barakos; Farhad Sahebkar
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  48     ISSN:  1873-5150     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2013 Mar 
Date Detail:
Created Date:  2013-02-19     Completed Date:  2013-08-05     Revised Date:  2013-11-01    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  244-8     Citation Subset:  IM    
Copyright Information:
Copyright © 2013 Elsevier Inc. All rights reserved.
Division of Pediatric Neurology, California Pacific Medical Center, San Francisco, California, USA.
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MeSH Terms
Brain Stem / pathology*
Diagnosis, Differential
Disease Progression
Encephalitis / diagnosis*,  drug therapy,  pathology
Fever / etiology,  pathology
Glucocorticoids / therapeutic use
Magnetic Resonance Imaging
Methylprednisolone / therapeutic use
Treatment Outcome
Reg. No./Substance:
0/Glucocorticoids; 83-43-2/Methylprednisolone
Comment In:
Pediatr Neurol. 2013 Oct;49(4):e9   [PMID:  23953997 ]

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