Document Detail


Rett syndrome: presumptive carriers of the gene defect. Sex ratio among their siblings.
MedLine Citation:
PMID:  9452931     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The live-born full siblings of 121 presumptive carriers of Rett syndrome belonging to eight pedigrees were examined as to sex ratio at birth. A total of 394 such siblings born in the period 1757-1966 were identified. 183 (46.4%) of them were male and 211 (53.6%) female, i.e., significantly fewer than in the average Swedish population (p = 0.03) were male. Our findings support the existence of one or more lethal alleles causing Rett syndrome.
Authors:
H O Akesson; B Hagberg; J Wahlström
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  European child & adolescent psychiatry     Volume:  6 Suppl 1     ISSN:  1018-8827     ISO Abbreviation:  Eur Child Adolesc Psychiatry     Publication Date:  1997  
Date Detail:
Created Date:  1998-05-06     Completed Date:  1998-05-06     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  9212296     Medline TA:  Eur Child Adolesc Psychiatry     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  101-2     Citation Subset:  IM    
Affiliation:
Department of Psychiatry, Sahlgren University Hospital, Göteborg, Sweden.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Binomial Distribution
Confidence Intervals
Female
Genes, Lethal
Heterozygote*
Humans
Male
Nuclear Family
Pedigree
Retrospective Studies
Rett Syndrome / epidemiology,  genetics*
Sex Ratio*
Sweden / epidemiology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Pedigree analysis of Hungarian Rett syndrome girls.
Next Document:  Rett syndrome: habilitation and management reviewed.