| Respiratory Failure of Williams-Campbell Syndrome is Effectively Treated by Noninvasive Positive Pressure Ventilation. | |
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MedLine Citation:
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PMID: 21841334 Owner: NLM Status: In-Data-Review |
Abstract/OtherAbstract:
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Williams-Campbell syndrome is a rare disease, characterized by a congenital deficiency of cartilage in the fourth to sixth order bronchi, leading to chronic respiratory failure with recurrent pulmonary infections. An effective and practical treatment has not yet been established. A 31-year-old man who was diagnosed as Williams-Campbell syndrome by inspiratory and expiratory computed tomography findings developed recurrent pulmonary infections and showed progressive deterioration of dyspnea. Domiciliary NPPV was administered, followed by a dramatic improvement of respiratory failure and a decrease in the episodes of pulmonary infections. NPPV may have an advantage in adults with Williams-Campbell syndrome who have severe respiratory failure and recurrent pulmonary infections. |
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Authors:
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Hiroshi Wada; Ruriko Seto; Hideto Yamada; Taishi Nagao; Takashi Hajiro; Yasutaka Nakano |
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Publication Detail:
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Type: Journal Article Date: 2011-08-15 |
Journal Detail:
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Title: Internal medicine (Tokyo, Japan) Volume: 50 ISSN: 1349-7235 ISO Abbreviation: Intern. Med. Publication Date: 2011 |
Date Detail:
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Created Date: 2011-08-15 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9204241 Medline TA: Intern Med Country: Japan |
Other Details:
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Languages: eng Pagination: 1729-32 Citation Subset: IM |
Affiliation:
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Division of Respiratory Medicine, Department of Internal Medicine, Shiga University of Medical Science, Japan. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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