Document Detail


Resolution of large azygos vein aneurysm following stent-graft shunt placement in a patient with Ehlers-Danlos syndrome type IV.
MedLine Citation:
PMID:  16252082     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Ehlers-Danlos syndrome (EDS) type IV is a rare connective tissue disorder associated with thin-walled, friable arteries and veins predisposing patients to aneurysm formation, dissection, fistula formation, and vessel rupture. Azygos vein aneurysm is an extremely rare condition which has not been reported in association with EDS in the literature. We present a patient with EDS type IV and interrupted inferior vena cava (IVC) with azygos continuation who developed an azygos vein aneurysm. In order to decrease flow through the azygos vein and reduce the risk of aneurysm rupture, a stent-graft shunt was created from the right hepatic vein to the azygos vein via a transhepatic, retroperitoneal route. At 6 month follow-up the shunt was open and the azygos vein aneurysm had resolved.
Authors:
Estelle S D'Souza; David M Williams; G M Deeb; Wojciech Cwikiel
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Cardiovascular and interventional radiology     Volume:  29     ISSN:  0174-1551     ISO Abbreviation:  Cardiovasc Intervent Radiol     Publication Date:    2006 Sep-Oct
Date Detail:
Created Date:  2006-07-26     Completed Date:  2006-12-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8003538     Medline TA:  Cardiovasc Intervent Radiol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  915-9     Citation Subset:  IM    
Affiliation:
Department of Radiology, University of Michigan Hospitals, 1500 E. Medical Center Drive, Ann Arbor, MI 48109-0030, USA.
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MeSH Terms
Descriptor/Qualifier:
Adult
Aneurysm / diagnosis,  therapy*
Azygos Vein* / pathology,  radiography
Blood Vessel Prosthesis Implantation*
Ehlers-Danlos Syndrome / complications*
Female
Hepatic Veins / radiography
Humans
Radiography, Interventional
Renal Veins / radiography
Stents*
Vena Cava, Inferior / pathology,  radiography

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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