Document Detail


Recurrent deep vein thrombosis and pulmonary embolism in a young man with Klinefelter's syndrome and heterozygous mutation of MTHFR-677C>T and 1298A>C.
MedLine Citation:
PMID:  20449891     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Klinefelter's syndrome is characterized by hypogonadism and infertility and commonly has an XXY karyotype. Within the population of men with this disorder, there is an increased incidence of venous thromboembolic disease. Although the precise mechanisms underlying this prothrombotic state have not been elucidated, it is thought that the increased incidence of thromboembolism is associated with a hypofibrinolytic state secondary to androgen deficiency. We present the case of a 26-year-old man with Klinefelter's syndrome who had recurrent episodes of deep venous thrombosis and pulmonary embolism while undergoing therapeutic anticoagulation. Coagulation studies were significant for the heterozygous mutations of MTHFR-677C>T and 1298A>C gene and hyperhomocystenemia. Our aim is to raise awareness of this association and discuss management for these patients.
Authors:
Joel R Angel; Stacey Parker; Ryan E Sells; Ehab Atallah
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Blood coagulation & fibrinolysis : an international journal in haemostasis and thrombosis     Volume:  21     ISSN:  1473-5733     ISO Abbreviation:  Blood Coagul. Fibrinolysis     Publication Date:  2010 Jun 
Date Detail:
Created Date:  2010-05-06     Completed Date:  2010-08-09     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9102551     Medline TA:  Blood Coagul Fibrinolysis     Country:  England    
Other Details:
Languages:  eng     Pagination:  372-5     Citation Subset:  IM    
Affiliation:
Department of Medicine, Medical College of Wisconsin, Milwaukee, USA. jangel@mcw.edu <jangel@mcw.edu>
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MeSH Terms
Descriptor/Qualifier:
Anticoagulants / therapeutic use
Heterozygote
Humans
Klinefelter Syndrome / complications*
Male
Methylenetetrahydrofolate Reductase (NADPH2) / genetics*
Mutation*
Pulmonary Embolism / complications*,  drug therapy
Venous Thrombosis / complications*,  drug therapy
Young Adult
Chemical
Reg. No./Substance:
0/Anticoagulants; EC 1.5.1.20/Methylenetetrahydrofolate Reductase (NADPH2)

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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