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Rare association of Turner syndrome with neurofibromatosis type 1 and tuberous sclerosis complex.
MedLine Citation:
PMID:  20680156     Owner:  NLM     Status:  In-Data-Review    
Abstract/OtherAbstract:
We report a rare association of Turner syndrome with both Neurofibromatosis type I and Tuberous Sclerosis. The patient had XOkaryotype with Turners stigmata and also had features of Neurofibromatosis 1 in the form of significant café-au-lait spots and Plexiform neurofibroma along with typical features of Tuberous Sclerosis complex. Pedigree analysis revealed that the elder brother of the proband in the family also suffered from Tuberous Sclerosis without the manifestation of Neurofibromatosis or any other genetic disorders. We hypothesize that these associations could be due to new independent mutations and also increased maternal and paternal age in a pre-disposition of Turner syndrome.
Authors:
Malini S Suttur; Savitha R Mysore; Balasundaram Krishnamurthy; Ramachandra B Nallur
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Indian journal of human genetics     Volume:  15     ISSN:  0971-6866     ISO Abbreviation:  Indian J Hum Genet     Publication Date:  2009 May 
Date Detail:
Created Date:  2010-08-03     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101223637     Medline TA:  Indian J Hum Genet     Country:  India    
Other Details:
Languages:  eng     Pagination:  75-7     Citation Subset:  -    
Affiliation:
Department of Studies in Zoology, Human Genetics Laboratory, University of Mysore, Manasagangothri, Mysore - 570 006, India.
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