Document Detail


Pure duplication 1q41-qter: further delineation of trisomy 1q syndromes.
MedLine Citation:
PMID:  18798309     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Several authors have attempted to characterize the partial 1q trisomy syndrome, reporting clinical features such as mental retardation, macrocephaly, large fontanels, prominent forehead, broad flat nasal bridge, high-arched palate, micro/retrognathia, low-set ears, and cardiac defects. However, defining the partial trisomy 1q syndrome is difficult, because it is a rare chromosomal abnormality and in most instances the trisomy 1q is combined with partial monosomy of another autosomal segment. We report on the clinical and molecular cytogenetic study of a patient who presents pure partial 1q duplication. This is the first case of pure duplication 1q41-qter in the literature.
Authors:
Leslie Domenici Kulikowski; Fernanda T S Bellucco; Sintia I Nogueira; Denise M Christofolini; Marilia de A C Smith; Claudia B de Mello; Decio Brunoni; Maria Isabel Melaragno
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  American journal of medical genetics. Part A     Volume:  146A     ISSN:  1552-4833     ISO Abbreviation:  Am. J. Med. Genet. A     Publication Date:  2008 Oct 
Date Detail:
Created Date:  2008-09-30     Completed Date:  2008-11-12     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101235741     Medline TA:  Am J Med Genet A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  2663-7     Citation Subset:  IM    
Copyright Information:
2008 Wiley-Liss, Inc.
Affiliation:
Department of Morphology and Genetics, Universidade Federal de São Paulo, São Paulo, SP, Brazil.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics
Child
Child, Preschool
Chromosome Aberrations*
Chromosome Banding
Chromosome Disorders / genetics*
Chromosome Painting
Chromosomes, Artificial, Bacterial
Chromosomes, Human, Pair 1 / genetics*
Cytogenetic Analysis
Humans
Infant
Infant, Newborn
Male
Mental Retardation / genetics
Syndrome
Trisomy / genetics*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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