Document Detail


Pulmonary thromboembolism associated with Klippel-Trenaunay syndrome.
MedLine Citation:
PMID:  16166386     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Klippel-Trenaunay syndrome (KTS) is a rare congenital anomaly characterized by unilateral limb overgrowth, venous varicosities, and capillary malformations (port wine stains) of the affected limb or limbs. Large venous malformations such as those observed in KTS are rare, and many physicians are unfamiliar with the potential complications, which include hypercoagulability, thrombosis, and pulmonary embolism (PE). As a result, patients may suffer from delayed diagnosis of a potentially life-threatening thromboembolic event. We present 2 cases of children with KTS complicated by PE, and we review the English-language literature regarding pathophysiologic features, interventions, and outcomes of PE in the setting of KTS among both pediatric and adult patients, with emphasis on issues relevant to pediatricians.
Authors:
Erin E Huiras; Cheryl J Barnes; Lawrence F Eichenfield; Andrew N Pelech; Beth A Drolet
Related Documents :
15007616 - Parkes weber or klippel-trenaunay syndrome? non-invasive diagnosis with mr projection a...
8229056 - A new neurocutaneous syndrome possibly related to ota's nevus.
15664776 - Migraine-like attacks in child with sturge-weber syndrome without facial nevus.
16035646 - Sturge weber syndrome.
21206686 - Chronic kidney disease in mayer-rokitansky-kuster-hauser syndrome.
16709496 - Peeling skin syndrome.
Publication Detail:
Type:  Case Reports; Journal Article     Date:  2005-09-15
Journal Detail:
Title:  Pediatrics     Volume:  116     ISSN:  1098-4275     ISO Abbreviation:  Pediatrics     Publication Date:  2005 Oct 
Date Detail:
Created Date:  2005-10-03     Completed Date:  2005-12-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0376422     Medline TA:  Pediatrics     Country:  United States    
Other Details:
Languages:  eng     Pagination:  e596-600     Citation Subset:  AIM; IM    
Affiliation:
Department of Pediatric Dermatology, Children's Hospital of Wisconsin, Medical College of Wisconsin, Milwaukee, Wisconsin, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Acute Disease
Adolescent
Child
Humans
Klippel-Trenaunay-Weber Syndrome / complications*
Leg
Male
Pulmonary Embolism / complications*
Venous Thrombosis / complications

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  The bromodomain protein GTE6 controls leaf development in Arabidopsis by histone acetylation at ASYM...
Next Document:  Quantification of neurocognitive changes before, during, and after hyperbaric oxygen therapy in a ca...