Document Detail


Pulmonary atresia/ventricular septal defect associated with facial port-wine stain and retinal vascular abnormality: a new constellation?
MedLine Citation:
PMID:  12966530     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A case with pulmonary atresia/ventricular septal defect associated with port-wine stain and retinal vascular abnormality is reported. Clinical findings were similar to both PHACE syndrome and Sturge-Weber syndrome (SWS). But, the most frequent and well-known features of both syndromes were absent. So, it could not be concluded whether this is a new constellation or an incomplete form of one of the two syndromes. In both situations, presence of a complex congenital heart disease that has not been reported previously makes this case original.
Authors:
Hüseyin Tan; Naci Ceviz; Orhan Baykal; Mustafa Büyükavci; Necmettin Bilici
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  American journal of medical genetics. Part A     Volume:  122A     ISSN:  1552-4825     ISO Abbreviation:  Am. J. Med. Genet. A     Publication Date:  2003 Oct 
Date Detail:
Created Date:  2003-09-10     Completed Date:  2004-04-22     Revised Date:  2008-05-21    
Medline Journal Info:
Nlm Unique ID:  101235741     Medline TA:  Am J Med Genet A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  266-8     Citation Subset:  IM    
Copyright Information:
Copyright 2003 Wiley-Liss, Inc.
Affiliation:
Department of Pediatric Neurology, Faculty of Medicine, Yakutiye Research Hospital, Atatürk University, 25240 Erzurum, Turkey. huseyin_tan@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / pathology*
Adolescent
Diagnosis, Differential
Eye Abnormalities / pathology*
Female
Heart Defects, Congenital / pathology*
Humans
Port-Wine Stain / pathology*
Pulmonary Atresia / pathology*
Syndrome
Comments/Corrections
Comment In:
Am J Med Genet A. 2005 Jan 30;132A(3):340-1   [PMID:  15690382 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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