Document Detail

Pulmonary circulation in pulmonary atresia associated with the asplenia cardiac syndrome.
MedLine Citation:
PMID:  1634672     Owner:  NLM     Status:  MEDLINE    
OBJECTIVE: The goal of this study was to determine the patterns of the pulmonary circulation in patients with pulmonary atresia and asplenia. BACKGROUND: The asplenic cardiac syndromes characteristically have complex cardiac anomalies including pulmonary stenosis or atresia. Definition of the pulmonary artery circulation and pulmonary venous connections is needed for consideration of surgical procedures. METHODS: In 35 patients, the sources of pulmonary blood flow, anatomic features of pulmonary arteries and pulmonary venous connections were determined from angiograms or autopsy specimens. RESULTS: The main pulmonary artery was absent or hypoplastic in 91% of patients; most had a ductus arteriosus. The right and left pulmonary arteries were confluent in 90% and usually of normal size (right 71%, left 63%). Total anomalous pulmonary venous connections were present in 38%. CONCLUSIONS: The anatomic features of the pulmonary arteries in pulmonary atresia associated with the asplenic cardiac syndrome are usually favorable for palliative surgical procedures. Total anomalous pulmonary venous connection may exist as a complicating factor.
R Vitiello; J H Moller; B Marino; U Vairo; J E Edwards; J L Titus
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Journal of the American College of Cardiology     Volume:  20     ISSN:  0735-1097     ISO Abbreviation:  J. Am. Coll. Cardiol.     Publication Date:  1992 Aug 
Date Detail:
Created Date:  1992-08-21     Completed Date:  1992-08-21     Revised Date:  2010-03-24    
Medline Journal Info:
Nlm Unique ID:  8301365     Medline TA:  J Am Coll Cardiol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  363-5     Citation Subset:  AIM; IM    
Department of Pediatrics, University of Minnesota, Minneapolis.
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MeSH Terms
Child, Preschool
Ductus Arteriosus, Patent / pathology
Heart Defects, Congenital / pathology*
Pulmonary Artery / abnormalities*
Pulmonary Valve / abnormalities*
Pulmonary Veins / abnormalities*
Spleen / abnormalities*

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