| Pulmonary capillary hemangiomatosis. A report of three cases and a review of the literature. | |
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MedLine Citation:
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PMID: 2675708 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension. At present, only eleven cases have been reported. This report describes the clinical and pathologic findings in three additional cases who presented to the University of Pittsburgh for heart-lung transplantation and integrates the clinical features of all fourteen cases. Clinically, this disorder should be suspected in a patient who presents with pulmonary hypertension, hemoptysis, a reticulonodular infiltrate on chest radiograph, a lung scan showing inhomogeneously enhanced perfusion (particularly in the lower lobes), and pulmonary angiography showing increased peripheral vascularity corresponding to both the radiographic infiltrate and the areas of enhanced perfusion on lung scan. Histologic features consist of nodular proliferation of capillary-sized vessels that infiltrate the pulmonary interstitium, vascular walls, and lumens as well as the alveolar septa. The vascular invasion results in a secondary veno-occlusive phenomenon that explains the clinical confusion with pulmonary veno-occlusive disease. |
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Authors:
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C N Faber; S A Yousem; J H Dauber; B P Griffith; R L Hardesty; I L Paradis |
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Publication Detail:
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Type: Case Reports; Journal Article; Research Support, U.S. Gov't, P.H.S.; Review |
Journal Detail:
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Title: The American review of respiratory disease Volume: 140 ISSN: 0003-0805 ISO Abbreviation: Am. Rev. Respir. Dis. Publication Date: 1989 Sep |
Date Detail:
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Created Date: 1989-10-19 Completed Date: 1989-10-19 Revised Date: 2007-11-14 |
Medline Journal Info:
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Nlm Unique ID: 0370523 Medline TA: Am Rev Respir Dis Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 808-13 Citation Subset: AIM; IM |
Affiliation:
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Department of Medicine, University of Pittsburgh, School of Medicine, Pennsylvania 15260. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Capillaries / pathology Female Hemangioma* / complications, pathology, radiography Humans Hypertension, Pulmonary / etiology Lung / blood supply, pathology, radiography Lung Neoplasms* / complications, pathology, radiography Middle Aged |
| Grant Support | |
ID/Acronym/Agency:
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HL-37553/HL/NHLBI NIH HHS |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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