Document Detail


Pulmonary atresia with intact ventricular septum: strategy based on right ventricular morphology.
MedLine Citation:
PMID:  14666014     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVES: Management strategy for pulmonary atresia with intact ventricular septum is controversial. We treated patients with this anomaly according to a management protocol based on our quantitative assessment of right ventricular morphology (index of right ventricular development and right ventricle-tricuspid valve index). In the present study, we reviewed a 20-year experience of the surgical treatment at our institution to define guidelines for selecting the appropriate type of surgical procedure. METHODS: Between April 1981 and June 2002, 45 consecutive patients with pulmonary atresia with intact ventricular septum underwent surgical treatment. Open transpulmonary valvotomy was performed in 27 patients and Blalock-Taussig shunt in 18 patients as the initial palliative procedure. Three patients who underwent a successful transpulmonary valvotomy alone in the neonatal period required no further operation. Definitive repair was performed in 32 patients. Biventricular repair was performed on 19 patients, one and a half ventricular repair in 3, and Fontan-type operation in 10. RESULTS: There were 1 early and 2 late deaths before the definitive operation in patients who underwent transpulmonary valvotomy. Two patients who had coronary artery interruption died 3 months and 13 years after the initial Blalock-Taussig shunt. There were 1 early and 2 late deaths after the definitive operation. Actuarial survival, including noncardiac death, was 91.1% at 5 years after the initial procedure and 81.5% at 10 years. CONCLUSIONS: We treated patients with pulmonary atresia with intact ventricular septum according to a management protocol based on our quantitative assessment of right ventricular morphology with good results.
Authors:
Naoki Yoshimura; Masahiro Yamaguchi; Hidetaka Ohashi; Yoshihiro Oshima; Shigeteru Oka; Masahiro Yoshida; Hirohisa Murakami; Teruo Tei
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Publication Detail:
Type:  Comparative Study; Journal Article    
Journal Detail:
Title:  The Journal of thoracic and cardiovascular surgery     Volume:  126     ISSN:  0022-5223     ISO Abbreviation:  J. Thorac. Cardiovasc. Surg.     Publication Date:  2003 Nov 
Date Detail:
Created Date:  2003-12-10     Completed Date:  2004-01-14     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0376343     Medline TA:  J Thorac Cardiovasc Surg     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1417-26     Citation Subset:  AIM; IM    
Affiliation:
Department of Cardiothoracic Surgery, Kobe Children's Hospital, Japan. y-naoki@za2.so-net.ne.jp
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MeSH Terms
Descriptor/Qualifier:
Cardiac Surgical Procedures / methods*,  mortality
Cohort Studies
Female
Follow-Up Studies
Fontan Procedure / methods,  mortality
Heart Catheterization / methods*
Heart Septum / anatomy & histology*
Heart Ventricles / surgery
Humans
Infant, Newborn
Male
Palliative Care / methods
Pulmonary Atresia / diagnosis*,  surgery*
Reference Values
Reoperation
Retrospective Studies
Risk Assessment
Severity of Illness Index
Survival Rate
Time Factors
Treatment Outcome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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