| Prune belly syndrome with pouch colon and absent dermatome. | |
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MedLine Citation:
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PMID: 20098006 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Prune belly syndrome (PBS) is a rare congenital constellation of defects in pediatric surgical practice. Although anorectal anomalies have been reported in association with PBS, only few case of pouch colon with PBS has been reported. [1] In addition, our patient had deficient abdominal wall with absent dermatome in left upper quadrant, which has never been reported in the English literature. This association with abdominal wall deficiency and absent dermatome not only strengthens the theory of mesodermal arrest in the etiology of PBS but also points towards a defect in the ectodermal development. |
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Authors:
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Aejaz A Baba; Syed A Hussain; Altaf H Shera; Rekha Patnaik |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: African journal of paediatric surgery : AJPS Volume: 7 ISSN: 0974-5998 ISO Abbreviation: Afr J Paediatr Surg Publication Date: 2010 Jan-Apr |
Date Detail:
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Created Date: 2010-01-25 Completed Date: 2010-04-05 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101255062 Medline TA: Afr J Paediatr Surg Country: Nigeria |
Other Details:
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Languages: eng Pagination: 25-7 Citation Subset: IM |
Affiliation:
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Department of Pediatric Surgery, SKIMS, Srinagar, Kashmir, India. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Abdominal Wall
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abnormalities Anal Canal / abnormalities* Colon / abnormalities*, surgery Colostomy Cystostomy Female Follow-Up Studies Humans Infant, Newborn Male Prune Belly Syndrome* / complications, surgery Rectum / abnormalities* Treatment Outcome Urinary Fistula / surgery |
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