| Proteus syndrome and immunodeficiency. | |
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MedLine Citation:
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PMID: 10685928 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 10 year old boy with Proteus syndrome presented with a pericardial effusion of unknown aetiology. Immunological investigation revealed low serum IgG and IgA, accompanied by low levels of specific antibodies to pneumococcal and haemophilus type B polysaccharides. Circulating lymphocyte surface marker profile revealed T and B cell lymphopenia. This is the first report of hypogammaglobulinaemia occurring in the Proteus syndrome. |
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Authors:
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D Hodge; S A Misbah; R F Mueller; E J Glass; P A Chetcuti |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Archives of disease in childhood Volume: 82 ISSN: 1468-2044 ISO Abbreviation: Arch. Dis. Child. Publication Date: 2000 Mar |
Date Detail:
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Created Date: 2000-03-16 Completed Date: 2000-03-16 Revised Date: 2009-11-18 |
Medline Journal Info:
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Nlm Unique ID: 0372434 Medline TA: Arch Dis Child Country: ENGLAND |
Other Details:
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Languages: eng Pagination: 234-5 Citation Subset: AIM; IM |
Affiliation:
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Department of Paediatrics and Child Health, University of Leeds, Leeds, UK. D.Hodge@leeds.ac.uk |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Agammaglobulinemia
/
blood,
complications*,
immunology Child Humans Immunoglobulin G / blood Lymphopenia / blood, complications*, immunology Male Pericardial Effusion / etiology*, immunology Proteus Syndrome / blood, complications*, immunology |
| Chemical | |
Reg. No./Substance:
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0/Immunoglobulin G |
| Comments/Corrections | |
Comment In:
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Arch Dis Child. 2000 Sep;83(3):276
[PMID:
10991755
]
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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