Document Detail


Progressive multifocal leukoencephalopathy associated with mycophenolate mofetil treatment in a woman with lupus and CD4+ T-lymphocyte deficiency.
MedLine Citation:
PMID:  21976399     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
There is an increase in the number of patients with systemic lupus erythematosus (SLE) reported as developing progressive multifocal leukoencephalopathy (PML) while on intensive immunosuppressive therapy. A 39-year-old HIV-negative woman with a 10-year history of SLE presented with progressive left-side weakness while on maintenance therapy with oral prednisone and mycophenolate mofetil (MMF). On several occasions low CD4+ T-lymphocyte counts were found (68/µL). Brain magnetic resonance imaging (MRI) revealed a large lesion in the right subcortical fronto-parietal region and a smaller one in the left frontal subcortex, corresponding to the PML. In cerebrospinal fluid, polymerase chain reaction (PCR) for JC virus (JCV) was negative, but anti-JCV antibodies were highly positive. Diagnosis of probable PML was made and MMF was withdrawn. The patient's condition improved with marked reduction of left-side weakness and an increase in CD4(+) T-lymphocyte count (141/µL). Follow-up MRI showed regression of lesions and over the next 6 months the patient remained stable. In spite of the grave prognosis associated with PML, SLE patients can have an excellent outcome if immunosuppressants are discontinued as soon as the correct diagnosis is made. SLE patients with associated low CD4(+) T-lymphocyte counts should be monitored for the development of PML during immunosuppressive therapy in particular.
Authors:
A M Pavlovic; B Bonaci-Nikolic; D Kozic; J Ostojic; M Abinun; T Svabic-Medjedovic; M Nikolic; N Sternic
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't     Date:  2011-10-05
Journal Detail:
Title:  Lupus     Volume:  21     ISSN:  1477-0962     ISO Abbreviation:  Lupus     Publication Date:  2012 Jan 
Date Detail:
Created Date:  2011-12-15     Completed Date:  2012-04-24     Revised Date:  2013-03-21    
Medline Journal Info:
Nlm Unique ID:  9204265     Medline TA:  Lupus     Country:  England    
Other Details:
Languages:  eng     Pagination:  100-2     Citation Subset:  IM    
Affiliation:
Clinic for Neurology, Faculty of Medicine, University of Belgrade, Belgrade, Serbia. aleksandrapavlovic@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Adult
CD4 Lymphocyte Count*
CD4-Positive T-Lymphocytes / cytology*,  metabolism*
Female
Humans
Immunosuppressive Agents / adverse effects*
JC Virus / physiology
Leukoencephalopathy, Progressive Multifocal / chemically induced*,  pathology,  virology
Lupus Erythematosus, Systemic / complications,  drug therapy*
Magnetic Resonance Imaging
Mycophenolic Acid / adverse effects,  analogs & derivatives*
Virus Activation
Chemical
Reg. No./Substance:
0/Immunosuppressive Agents; 128794-94-5/mycophenolate mofetil; 24280-93-1/Mycophenolic Acid
Comments/Corrections
Comment In:
Z Rheumatol. 2013 Feb;72(1):5

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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