| Progressive discrete subaortic stenosis developed after successful primary repair of the supravalvular aortic stenosis in Williams syndrome. | |
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MedLine Citation:
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PMID: 19653183 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Discrete subaortic stenosis is a rare, late complication of the surgical repair of congenital heart defects. Secondary subaortic stenosis late after surgical repair of supravalvular aortic stenosis in Williams syndrome has not previously been described. A 20 year-old female patient with Williams syndrome became symptomatic eight years after subaortic membrane resection. A discrete subaortic stenosis was identified by echocardiography. She was indicated for a Konno operation with a 19-mm Sorin SL valve inserted in the aortic position, along with ventricular septal defect closure with a pericardial patch. She produced a transient slight hypocalcemia after the operation. She was discharged home in a good condition on the fourth post-operative day. Intracardiac morphological and hemodynamic factors have been suggested as responsible for such a late complication. Our case study suggests the need for regular follow-up in patients with Williams syndrome, even after primary surgical repair. |
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Authors:
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Shi-Min Yuan; Rafael Kuperstein; Jacob Lavce |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Cardiology journal Volume: 16 ISSN: 1897-5593 ISO Abbreviation: - Publication Date: 2009 |
Date Detail:
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Created Date: 2009-08-04 Completed Date: 2009-10-21 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101392712 Medline TA: Cardiol J Country: Poland |
Other Details:
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Languages: eng Pagination: 368-71 Citation Subset: IM |
Affiliation:
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Departments of Cardiac and Thoracic Surgery, The Chaim Sheba Medical Center, Tel Hashomer, Israel. shi_min_yuan@yahoo.com |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Aortic Stenosis, Supravalvular
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etiology,
surgery* Discrete Subaortic Stenosis / etiology*, ultrasonography Disease Progression Echocardiography Female Humans Postoperative Complications* Williams Syndrome / complications* Young Adult |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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