Document Detail


Progressive Hemifacial Atrophy--case report.
MedLine Citation:
PMID:  16505785     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Progressive Hemifacial Atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive atrophy affecting one side of the face. The incidence and the cause of this alteration is unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. This can be the result of a trophic malformation of Cervical Sympathetic Nervous System. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity, among others. The most common complications that appear in association to this health disorder are: trigeminal neuritis, facial paresthesia, severe headache and epilepsy, being this last one the most frequent complication of the Central Nervous System. Characteristically, the atrophy progresses slowly for several years and, soon after, it become stable. Now, plastic surgery with graft of autogenous fat can be performed, after stabilization of the disease, to correct the deformity. Orthodontic treatment can help in the correction of any associated malformation. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology, differential diagnosis and treatment of progressive hemifacial atrophy.
Authors:
Thiago Pastor da Silva Pinheiro; Camila Camarinha da Silva; Carolina Souza Limeira da Silveira; Patrícia Cristina Ereno Botelho; Maria das Graças Rodriguez Pinheiro; João de Jesus Viana Pinheiro
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Publication Detail:
Type:  Case Reports; Journal Article; Review     Date:  2006-03-01
Journal Detail:
Title:  Medicina oral, patología oral y cirugía bucal     Volume:  11     ISSN:  1698-6946     ISO Abbreviation:  Med Oral Patol Oral Cir Bucal     Publication Date:  2006 Mar 
Date Detail:
Created Date:  2006-02-28     Completed Date:  2006-07-13     Revised Date:  2009-12-11    
Medline Journal Info:
Nlm Unique ID:  101231694     Medline TA:  Med Oral Patol Oral Cir Bucal     Country:  Spain    
Other Details:
Languages:  eng     Pagination:  E112-4     Citation Subset:  D; IM    
Affiliation:
Department of Estomatology, School of Dentistry, University Center of Pará, Brazil.
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MeSH Terms
Descriptor/Qualifier:
Child
Disease Progression
Facial Hemiatrophy* / diagnosis,  etiology,  physiopathology,  therapy
Female
Humans

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