Document Detail


Profuse Congenital Familial Milia with Absent Dermatoglyphics (Basan's Syndrome): Description of a New Family.
MedLine Citation:
PMID:  21906143     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
  Milia are common, small, keratin-containing cysts frequently seen in all age groups. They may arise spontaneously or develop after a variety of stimuli. They can be found alone or as part of syndromes. We present a female neonate born not only with profuse facial milia, but also with acral bullae and absent dermatoglyphics. Similar features were seen in several members of her family. These findings correspond to the syndrome known as Basan's syndrome, a rare autosomal-dominant inherited dermatosis characterized by profuse congenital milia, transient neonatal acral bullae, and absence of dermatoglyphics.
Authors:
Paula Carolina Luna; Margarita Larralde
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2011-9-9
Journal Detail:
Title:  Pediatric dermatology     Volume:  -     ISSN:  1525-1470     ISO Abbreviation:  -     Publication Date:  2011 Sep 
Date Detail:
Created Date:  2011-9-12     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8406799     Medline TA:  Pediatr Dermatol     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Copyright Information:
© 2011 Wiley Periodicals, Inc.
Affiliation:
Dermatology Department, Hospital Alemán, Buenos Aires, Argentina Pediatric Dermatology Section, Hospital Ramos Mejía, Buenos Aires, Argentina.
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