| Primary localized cutaneous nodular amyloidosis and CREST syndrome: a case report and review of the literature. | |
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MedLine Citation:
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PMID: 18712025 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Primary localized cutaneous nodular amyloidosis (PLCNA) is a form of primary localized cutaneous amyloidosis (PLCA) that presents as yellowish waxy nodules on the extremities, face, trunk, or genitalia. We report the case of a patient with PLCNA and CREST (calcinosis, Raynaud phenomenon, esophageal motility disorders, sclerodactyly, and telangiectasia) syndrome. A diagnosis of her extensive PLCNA was made after biopsy specimens from the bilateral shins stained positive for amyloid extending from the superficial papillary dermis to the subcutis. Results of a workup were negative for paraproteinemia or signs of systemic amyloidosis and have remained so after 8 years of follow-up. We present a review of the literature describing the presentation and histopathology of the varying forms of amyloidosis. |
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Authors:
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Erika M Summers; Christina G Kendrick |
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Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: Cutis; cutaneous medicine for the practitioner Volume: 82 ISSN: 0011-4162 ISO Abbreviation: Cutis Publication Date: 2008 Jul |
Date Detail:
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Created Date: 2008-08-20 Completed Date: 2008-10-30 Revised Date: 2009-11-11 |
Medline Journal Info:
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Nlm Unique ID: 0006440 Medline TA: Cutis Country: United States |
Other Details:
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Languages: eng Pagination: 55-9 Citation Subset: IM |
Affiliation:
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Department of Internal Medicine, Harvard Medical Faculty Physicians, Beth Israel Deaconess Medical Center, Boston, MA 02215, USA. esummers@bidmc.harvard.edu |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Amyloidosis
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complications*,
pathology*,
therapy CREST Syndrome / complications*, pathology*, therapy Female Humans Middle Aged Skin Diseases, Metabolic / complications*, pathology*, therapy |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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